Familial progressive vestibulocochlear dysfunction.
A kindred is presented in which several members had complaints of head movement-dependent oscillopsia due to acquired vestibular areflexia in combination with progressive hearing loss. History was noncontributory for other neurologic or otologic diseases (including infectious diseases) or use of neuro-ototoxic drugs. The pedigree suggests autosomal dominant inheritance.
Verhagen
W I
WI
Department of Neurology, Canisius-Wilhelmina Hospital, Nijmegen, the Netherlands.
Huygen
P L
PL
Joosten
E M
EM
D000368:Aged; D000369:Aged, 80 and over; D001299:Audiometry; D003051:Cochlea; D006311:Hearing Disorders / Q000150:complications; D006801:Humans; D007766:Lacrimal Apparatus Diseases / Q000150:complications / Q000235:genetics / Q000503:physiopathology; D008297:Male; D008875:Middle Aged; D009801:Oculomotor Muscles / Q000503:physiopathology; D010375:Pedigree; D014724:Vestibular Function Tests; D014722:Vestibule, Labyrinth