[Arrhythmogenic right ventricular dysplasia. Study of a selected population].
268 patients (pts) aged between 4 and 63 (average block 33.6) years were examined in an effort to detect structural and/or wall motion abnormalities of the right ventricle, consistent with a diagnosis of Arrhythmogenic Right Ventricular Dysplasia (ARVD). The patients included in this study had some of these features: 1) sudden juvenile death (age less than 35 years) due to heart disease; 2) relatives of pts died suddenly of pathologically proven ARVD; 3) pts with ventricular arrhythmias grade Lown greater than 3, and with QRS morphology mainly of left bundle branch block; 4) pts between the ages of 18 and 40, with negative T waves beyond V2; 5) pts with ventricular arrhythmias of left bundle branch block morphology, and grade Lown greater than 1, and negative T waves beyond V1. ARVD was recognized in 108 living and 18 deceased pts. Our data confirm that ARVD is a wide spectrum disease, going from the classical form described by Marcus and Fontaine to concealed forms characterized mainly by premature ventricular complexes.
Nava
A
A
Cattedra e Divisione di Cardiologia, Università di Padova.
Martini
B
B
Thiene
G
G
Buja
G F
GF
Canciani
B
B
Scognamiglio
R
R
Miraglia
G
G
Corrado
D
D
Boffa
G M
GM
Daliento
L
L
D000293:Adolescent; D000328:Adult; D000367:Age Factors; D001145:Arrhythmias, Cardiac / Q000209:etiology* / Q000235:genetics / Q000401:mortality; D002648:Child; D002675:Child, Preschool; D002986:Clinical Trials as Topic; D003645:Death, Sudden / Q000209:etiology; D004562:Electrocardiography; D005260:Female; D005500:Follow-Up Studies; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D008297:Male; D008875:Middle Aged; D009200:Myocardial Contraction
La displasia aritmogena del ventricolo destro. Studio su una popolazione selezionata.