title: [Arrhythmogenic right ventricular dysplasia. Study of a selected population].
abstract: 268 patients (pts) aged between 4 and 63 (average block 33.6) years were examined in an effort to detect structural and/or wall motion abnormalities of the right ventricle, consistent with a diagnosis of Arrhythmogenic Right Ventricular Dysplasia (ARVD). The patients included in this study had some of these features: 1) sudden juvenile death (age less than 35 years) due to heart disease; 2) relatives of pts died suddenly of pathologically proven ARVD; 3) pts with ventricular arrhythmias grade Lown greater than 3, and with QRS morphology mainly of left bundle branch block; 4) pts between the ages of 18 and 40, with negative T waves beyond V2; 5) pts with ventricular arrhythmias of left bundle branch block morphology, and grade Lown greater than 1, and negative T waves beyond V1. ARVD was recognized in 108 living and 18 deceased pts. Our data confirm that ARVD is a wide spectrum disease, going from the classical form described by Marcus and Fontaine to concealed forms characterized mainly by premature ventricular complexes.
authors.affiliation: Cattedra e Divisione di Cardiologia, Università di Padova.
authors.forename: A
authors.initials: A
authors.lastname: Nava
authors.forename: B
authors.initials: B
authors.lastname: Martini
authors.forename: G
authors.initials: G
authors.lastname: Thiene
authors.forename: G F
authors.initials: GF
authors.lastname: Buja
authors.forename: B
authors.initials: B
authors.lastname: Canciani
authors.forename: R
authors.initials: R
authors.lastname: Scognamiglio
authors.forename: G
authors.initials: G
authors.lastname: Miraglia
authors.forename: D
authors.initials: D
authors.lastname: Corrado
authors.forename: G M
authors.initials: GM
authors.lastname: Boffa
authors.forename: L
authors.initials: L
authors.lastname: Daliento
mesh_terms: D000293:Adolescent; D000328:Adult; D000367:Age Factors; D001145:Arrhythmias, Cardiac / Q000209:etiology* / Q000235:genetics / Q000401:mortality; D002648:Child; D002675:Child, Preschool; D002986:Clinical Trials as Topic; D003645:Death, Sudden / Q000209:etiology; D004562:Electrocardiography; D005260:Female; D005500:Follow-Up Studies; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D008297:Male; D008875:Middle Aged; D009200:Myocardial Contraction
vernacular_title: La displasia aritmogena del ventricolo destro. Studio su una popolazione selezionata.