[Panencephalopathy of the Creutzfeldt-Jakob disease type].
Creutzfeldt-Jakob disease (CJD) occurring in later life has a duration of about one year. Gait disturbance, myoclonic jerks, dementia and akinetic mutism occur. Post-mortem examination of the brain shows nerve cell loss, gliosis and spongiform changes of the grey matter. Clinical and neuropathological features of a case of the panencephalopathic type of CJD, with additional extensive degeneration of the cerebral white matter, are described. The panencephalopathic type of CJD is characterized clinically by a longer duration and a biphasic course.
Gertz
H J
HJ
Institut für Neuropathologie, Klinikum Steglitz der Freien Universität Berlin.
Stoltenburg
G
G
Cruz-Sanchez
F
F
Lafuente
J
J
Schopol
R
R
D000328:Adult; D001284:Atrophy; D001921:Brain / Q000473:pathology*; D002540:Cerebral Cortex / Q000473:pathology; D007562:Creutzfeldt-Jakob Syndrome / Q000473:pathology*; D005260:Female; D006801:Humans; D009186:Myelin Sheath / Q000648:ultrastructure; D009457:Neuroglia / Q000473:pathology; D009474:Neurons / Q000473:pathology; D013116:Spinal Cord / Q000473:pathology; D014057:Tomography, X-Ray Computed
Der panenzephalopathische Typ der Creutzfeldt-Jakob-Krankheit.