[Indications for liver transplantation in Wilson's disease].
We report the case of a 12 year-old boy with Wilson's disease, presenting with decompensated liver cirrhosis. Medical treatment failed to prevent fulminant liver failure in less than one month. Emergency liver transplantation was successfully performed. This report led us to review the prognosis of Wilson's disease with liver failure according to the present results of liver transplantation.
Gottrand
F
F
Service de Génétique et Maladies Héréditaires du Métabolisme de l'Enfant, Hôpital Huriez, CHR, Lille.
Razemon
M
M
Otte
J B
JB
Vigier
J E
JE
Farriaux
J P
JP
D000293:Adolescent; D004630:Emergencies; D006527:Hepatolenticular Degeneration / Q000150:complications / Q000601:surgery*; D006801:Humans; D008103:Liver Cirrhosis / Q000209:etiology* / Q000601:surgery; D016031:Liver Transplantation; D008297:Male; D011379:Prognosis
Indications de la transplantation hépatique au cours d'une maladie de Wilson.