[Budd-Chiari syndrome and Behçet's disease. A case treated by mesenterico-atrial prosthesis].
A 36 year-old North African man, with Behçet's syndrome complicated by an inferior vena caval thrombosis, developed a chronic Budd-Chiari syndrome associated with bleeding esophageal varices. He was treated by an emergency mesoatrial shunt. Results at 2 years were good. Analysis of this case and the 13 other similar cases with associated Budd-Chiari syndrome and Behçet's syndrome found in the literature showed that hepatic veins thrombosis: a) is often due to inferior vena caval thrombosis or membranous obstruction; b) has a high spontaneous mortality rate by acute liver failure; c) remains a potential indication for porto-systemic shunt, as are other causes of Budd-Chiari syndrome.
Le Treut
Y P
YP
Service de Chirurgie Digestive, Hôpital de la Conception, Marseille.
Comiti
Y
Y
Bremondy
A
A
Magnan
P E
PE
Raoult
D
D
Botta
D
D
Bricot
R
R
D000328:Adult; D001528:Behcet Syndrome / Q000150:complications*; D001807:Blood Vessel Prosthesis; D006502:Budd-Chiari Syndrome / Q000209:etiology / Q000601:surgery*; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011170:Portasystemic Shunt, Surgical
Syndrome de Budd-Chiari et maladie de Behçet. Une observation traitée par prothèse mésentérico-atriale.