Partially unroofed coronary sinus associated with tricuspid atresia. An important associated lesion in the Fontan operation.
A case of tricuspid atresia associated with partially unroofed coronary sinus following a Fontan operation is described. A 4-year-old boy with tricuspid atresia showed persistent arterial desaturation immediately after a modified Fontan operation. At reoperation on the next day, a partially unroofed coronary sinus was recognized and repaired through a left atriotomy. Although uncommon, this associated anomaly should be kept in mind even in the absence of a persistent left superior vena cava and should be suspected if arterial desaturation occurs after a modified Fontan operation.
Matsuwaka
R
R
Division of Cardiovascular Surgery, Osaka University Medical School, Japan.
Tomokuni
T
T
Ishikawa
S
S
Watanabe
F
F
Matsushita
T
T
Matsuda
H
H
D002675:Child, Preschool; D003330:Coronary Vessel Anomalies / Q000150:complications* / Q000601:surgery; D006344:Heart Septal Defects, Atrial / Q000601:surgery*; D006801:Humans; D008297:Male; D014261:Tricuspid Valve / Q000002:abnormalities*; D014680:Veins / Q000002:abnormalities