[Cubital dimelia. Apropos of a case with review of the literature].
Cubital or ulnar dimelia is a very rare congenital abnormality involving almost perfect duplication of the ulnar with absence of the radius, thumb and polydactyly. An eleven week old child was seen in the Department of Pediatric Surgery for a malformation of the left upper limb including deformity of the forearm with almost doubling of the hand and seven fingers. Radiological investigation revealed duplication of the ulna as well as of the metacarpals and fingers with absence of the radius and thumb. This type of abnormality remains controversial but clinical and radiological examination led to the conclusion of primary ulnar dimelia. We report a new case of this very rare congenital abnormality which was not accompanied by any other malformation.
Hinojosa
J F
JF
Service de Chirurgie Pédiatrique A., Hôpital d'enfants, Vandoeuvre-Les-Nancy.
Lascombes
P
P
Prevot
J
J
D006228:Hand Deformities, Congenital / Q000000981:diagnostic imaging*; D006801:Humans; D007223:Infant; D008297:Male; D011859:Radiography; D011884:Radius / Q000002:abnormalities / Q000000981:diagnostic imaging; D013933:Thumb / Q000002:abnormalities; D014457:Ulna / Q000002:abnormalities / Q000000981:diagnostic imaging
La dimélie cubitale. A propos d'un cas avec revue de la littérature.