[Linear sebaceous nevus syndrome].
We report a patient that fulfills the clinical features of the linear nevus sebaceous syndrome. This syndrome was defined by the triad: Linear nevus sebaceous, seizures and mental retardation. Further descriptions suggested an association with hamartomas of mesenchymal structures and increased risk of neoplasm transformation. Previously reported cases are reviewed. The complexity of classification of this neurocutaneous syndrome is discussed.
Pujol
R M
RM
Unidad de Neuropediatría, Clínica Infantil, Residencia Sanitaria Valle de Hebrón, Barcelona.
Tuneu
A
A
De Moragas
J M
JM
Tallada
M
M
Moreno
A
A
D005153:Facial Neoplasms / Q000473:pathology*; D006801:Humans; D007223:Infant; D008607:Intellectual Disability / Q000209:etiology*; D008297:Male; D009508:Nevus, Pigmented / Q000473:pathology*; D012640:Seizures / Q000209:etiology*; D013577:Syndrome
Síndrome del nevus sebáceo lineal.