[Adenocarcinoma of the cervix in Peutz-Jeghers syndrome. Case report and review of the literature].
The incidental finding of "adenoma malignum" or minimal deviation adenocarcinoma (MDA) of the cervix in a 38-year-old woman with Peutz-Jeghers syndrome (PJS) is reported and the literature is discussed. This highly differentiated form of adenocarcinoma is extremely rare but, like some other rare neoplasms, may occur more frequently in patients with PJS syndrome. Since the prognosis of MDA is considered poor and the histological diagnosis is often missed on biopsy, the importance of closely correlating clinical and pathological findings is emphasized.
von Hochstetter
A R
AR
Institut für Pathologie, Universitätsspital Zürich.
Ess
D
D
Bannwart
F
F
Bühler
H
H
D000230:Adenocarcinoma / Q000453:epidemiology* / Q000473:pathology; D000328:Adult; D005260:Female; D006801:Humans; D008875:Middle Aged; D010580:Peutz-Jeghers Syndrome / Q000150:complications* / Q000473:pathology; D011379:Prognosis; D002583:Uterine Cervical Neoplasms / Q000453:epidemiology* / Q000473:pathology
Adenokarzinom der Zervix bei Peutz-Jeghers-Syndrom. Fallbericht und Literaturübersicht.