title: [Primary pulmonary arterial hypertension].
abstract: Primary pulmonary hypertension (PPH) currently remains an entity of which the precise mechanism, most likely vasospastic, is not completely explained. The diagnosis of PPH remains an exclusion diagnosis; it will be considered only after ruling out a secondary pulmonary hypertension. Non-invasive techniques such as sonography, cardiac Doppler should permit an earlier diagnosis and an easier monitoring of these patients whose prognosis remains poor in spite of the sporadic efficacy of a treatment with vasodilators. Heart-Lung transplant could be a future prospect; however, if the first reports seem encouraging, the follow-up is currently insufficient to appreciate the possible long-term advantage.
authors.forename: F
authors.initials: F
authors.lastname: Chague
authors.forename: R
authors.initials: R
authors.lastname: Roudaut
authors.forename: M
authors.initials: M
authors.lastname: Dallocchio
mesh_terms: D003937:Diagnosis, Differential; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis* / Q000628:therapy; D013997:Time Factors
vernacular_title: Hypertension artérielle pulmonaire primitive.