Vegetating cicatricial pemphigoid. A new subset of the cicatricial pemphigoid spectrum.
A case with widespread vegetating-pustular skin lesions, oral erosions, ulcerations and scarring, and conjunctival synechiae is reported. Clinically, histopathologically, and by immunofluorescence and electron microscopy this patient combined the features of pemphigoid vegetans, as described by Winkelmann and Su, and the mucocutaneous type of cicatricial pemphigoid. This observation suggests that a third subset of cicatricial pemphigoid can now be added to the two existing ones, the mucocutaneous and Brunsting-Perry types, and the designation vegetating cicatricial pemphigoid is proposed for this heretofore undescribed condition.
Wolff
K
K
Department of Dermatology I, University of Vienna, Austria.
Rappersberger
K
K
Steiner
A
A
Konrad
K
K
D000368:Aged; D003937:Diagnosis, Differential; D005260:Female; D005455:Fluorescent Antibody Technique; D006801:Humans; D010390:Pemphigoid, Benign Mucous Membrane / Q000145:classification / Q000276:immunology / Q000473:pathology*; D012872:Skin Diseases, Vesiculobullous / Q000473:pathology*