title: [Orbital localization of clear-cell sarcoma of tendons and aponeuroses. Apropos of a case report].
abstract: Clear cell sarcoma of tendons and aponeuroses actually is a well identified soft tissue tumor. A primary orbital involvement is presented, with an optical and electron microscopic study. The orbital topography of such a tumor seems to be an exceptional opportunity. The histological study showed the typical pattern of this clear cell tumor. Ultrastructurally, there are not absolute specific features to establish the diagnosis, except the finding of intra-cellular melanosomes. Histogenesis has been debated for a long time between a melanotic or a synovial origin. According to present knowledge, this tumor may be attributed to a neural crest origin.
authors.affiliation: Service d'Ophtalmologie, Hôtel Dieu, Paris.
authors.forename: F
authors.initials: F
authors.lastname: D'Hermies
authors.forename: P
authors.initials: P
authors.lastname: Dhermy
authors.forename: C
authors.initials: C
authors.lastname: Clay
authors.forename: J
authors.initials: J
authors.lastname: Cophignon
authors.forename: M
authors.initials: M
authors.lastname: Savoldelli
authors.forename: Y
authors.initials: Y
authors.lastname: Pouliquen
mesh_terms: D000328:Adult; D005094:Exophthalmos / Q000209:etiology; D006801:Humans; D008297:Male; D009918:Orbital Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000648:ultrastructure; D012509:Sarcoma / Q000175:diagnosis / Q000473:pathology* / Q000648:ultrastructure; D013710:Tendons / Q000473:pathology* / Q000648:ultrastructure; D014463:Ultrasonography
vernacular_title: Localisation orbitaire d'un sarcome à cellules claires des tendons et aponévroses. A propos d'une observation.