Assay of acyl-CoA dehydrogenases in muscle and liver and identification of four new cases of medium-chain acyl-CoA dehydrogenase deficiency associated with systemic carnitine deficiency.
Zierz
S
S
University Neurology Clinic, Bonn, West Germany.
Engel
A G
AG
Romshe
C A
CA
D042964:Acyl-CoA Dehydrogenase; D044944:Acyl-CoA Dehydrogenases / Q000032:analysis* / Q000172:deficiency*; D002331:Carnitine / Q000172:deficiency*; D004579:Electron Transport; D006801:Humans; D008055:Lipids / Q000032:analysis; D008930:Mitochondria, Liver / Q000201:enzymology*; D008931:Mitochondria, Muscle / Q000201:enzymology*; D013379:Substrate Specificity
D008055:Lipids; D044944:Acyl-CoA Dehydrogenases; D042964:Acyl-CoA Dehydrogenase; D002331:Carnitine