title: Fontan repair for tricuspid atresia: experience with 50 consecutive patients.
abstract: From April, 1975, to October, 1985, 50 patients (mean age, 5.3 years; range, 2.5 to 14 years) underwent a Fontan repair for tricuspid atresia or severe tricuspid stenosis. Fifty-six palliative operations had been performed previously in 43 patients. Twenty-nine patients received an atriopulmonary connection by direct anastomosis [19], interposition of an aortic homograft [7], or a porcine heterograft [3]. An atrium-subpulmonary chamber connection was performed in 21 patients (Björk modification, 10; Dacron tube, 10; valved conduit, 1). Eleven patients (22%) died early, 6 of whom did not meet the established criteria for a Fontan operation. One patient died 6 months postoperatively of superior vena cava thrombosis. Four patients were reoperated on successfully. At a mean follow-up of 28.8 months, 28 patients are in New York Heart Association Functional Class I and 9 are in Class II; 1 patient was lost to follow-up. Thirteen patients underwent control catheterization fifteen days to four years postoperatively (median right atrial pressure, 14 mm Hg). Exercise testing in 9 asymptomatic patients, performed after a mean interval of 33 months, showed a moderate impairment of cardiac performance. We conclude that in select patients, a Fontan repair appears to be a reliable procedure at medium-term follow-up.
authors: Department of Cardiac Surgery, Ospedali Riuniti, Bergamo, Italy.
authors: F P
authors: FP
authors: Annecchino
authors: F
authors: F
authors: Brunelli
authors: A
authors: A
authors: Borghi
authors: P
authors: P
authors: Abbruzzese
authors: M
authors: M
authors: Merlo
authors: L
authors: L
authors: Parenzan
mesh_terms: D000293:Adolescent; D006328:Cardiac Catheterization; D002648:Child; D002675:Child, Preschool; D005080:Exercise Test; D005260:Female; D005500:Follow-Up Studies; D006352:Heart Ventricles / Q000503:physiopathology; D006801:Humans; D007223:Infant; D008297:Male; D008722:Methods; D011183:Postoperative Complications / Q000401:mortality; D011652:Pulmonary Circulation; D012086:Reoperation; D014261:Tricuspid Valve / Q000002:abnormalities* / Q000601:surgery