Epilepsy with bilateral occipital calcifications: a benign onset with progressive severity.
We studied four patients with a focal epilepsy and bilateral occipital corticosubcortical calcifications without any sign of phakomatosis. The clinical course of the disease was similar in all the patients and evolved from a benign onset to a severe encephalopathy with progressive mental impairment. The question of whether these patients have an incomplete and atypical form of Sturge-Weber syndrome or a previously undescribed disorder is addressed.
Gobbi
G
G
Department of Child Neurology, University of Bologna Medical School, Italy.
Sorrenti
G
G
Santucci
M
M
Rossi
P G
PG
Ambrosetto
P
P
Michelucci
R
R
Tassinari
C A
CA
D000293:Adolescent; D000328:Adult; D001927:Brain Diseases / Q000150:complications* / Q000503:physiopathology; D002114:Calcinosis / Q000150:complications* / Q000503:physiopathology; D004827:Epilepsy / Q000150:complications* / Q000503:physiopathology; D005260:Female; D006801:Humans; D008297:Male; D009778:Occipital Lobe / Q000503:physiopathology