Pulmonary telangiectasia without hypoxemia.
We describe an elderly patient with an unusual presentation of hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber disease) involving the lung. He had recurrent "pneumonia" caused by massive hemorrhage from endobronchial telangiectases. When stable, he was normoxic, had no evidence of right-to-left shunting, and had mild pulmonary arterial hypertension. His pulmonary telangiectases may be isolated to the bronchial circulation. We report hemodynamic data and show the first photographs of endobronchial telangiectases.
Lincoln
M J
MJ
Pulmonary Section, Veterans Administration Medical Center, Salt Lake City 84148.
Shigeoka
J W
JW
D000368:Aged; D001980:Bronchi / Q000098:blood supply; D001999:Bronchoscopy; D006801:Humans; D000860:Hypoxia; D008297:Male; D011652:Pulmonary Circulation; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000175:diagnosis*