[Budd-Chiari syndrome secondary to thrombosis of the inferior vena cava in myeloproliferative disease].
A case with abdominal pain, hepatosplenomegaly and ascites is reported. Ultrasonography and computed tomography showed a thrombus localized in the inferior vena cava at the confluence of the hepatic veins. The diagnosis of Budd-Chiari syndrome was made two years after clinical and laboratory findings appeared. The patient was affected by a Philadelphia-positive myeloproliferative disease that was the predisposing condition to the inferior vena cava thrombosis. We suggest that the diagnosis of Budd-Chiari syndrome must be considered in patients presenting conditions associated with thrombotic diathesis: so a suitable therapy can be started before an irreversible hepatic damage.
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Divisione Medica III, U.S.S.L. 75/1, Milano, Presidio Multizonale Ospedaliero dell'E.R.S.Z.
Ungaro
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D000368:Aged; D006502:Budd-Chiari Syndrome / Q000000981:diagnostic imaging / Q000209:etiology*; D005260:Female; D006801:Humans; D055728:Primary Myelofibrosis / Q000150:complications* / Q000473:pathology; D013927:Thrombosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000209:etiology; D014057:Tomography, X-Ray Computed; D014682:Vena Cava, Inferior
Sindrome di Budd-Chiari secondaria a trombosi della vena cava inferiore in corso di malattia mieloproliferativa.