Hearing loss in myotonic dystrophy.
Seventeen of 25 patients with myotonic dystrophy had moderate to severe hearing loss, usually sensorineural, that was identified by routine audiometric screening and was treatable in some patients. Further testing failed to reveal a single pathophysiological process.
Wright
R B
RB
Department of Neurology, Rush Medical College, Chicago, IL.
Glantz
R H
RH
Butcher
J
J
D000158:Acoustic Impedance Tests; D000293:Adolescent; D000328:Adult; D000368:Aged; D001301:Audiometry, Pure-Tone; D001933:Brain Stem / Q000503:physiopathology; D002648:Child; D002675:Child, Preschool; D005072:Evoked Potentials, Auditory; D006319:Hearing Loss, Sensorineural / Q000209:etiology*; D006801:Humans; D008875:Middle Aged; D009224:Myotonia Congenita / Q000150:complications / Q000503:physiopathology; D009223:Myotonic Dystrophy / Q000150:complications* / Q000503:physiopathology