title: [Clinical aspects, classification and prognosis of 7 cases of pediatric fibromatosis].
abstract: Seven cases of fibromatoses in infancy and childhood serve as examples to demonstrate this group of rare tumours, taking especially the aggressive forms of juvenile fibromatoses into account. There is a tendency to locally invasive destructive growth without metastasising at any time and a markedly high relapse rate after surgery--a tendency that showed up clearly in our patients, too. Only one child out of four having infantile (desmoid-type) fibromatosis of different localisation did not show any recurrence. The article reports, among other cases, on a desmoid of the stomach and oesophagus in a 15-year-old girl, not described in the literature so far, and on a congenital fibromatosis of the pancreas. Several classifications had to be performed to properly grade the individual cases (1, 6), since no generally valid systematic description of these tumours exists.
authors: Kinderchirurgische Klinik des Kinderkrankenhauses der Stadt Köln.
authors: B M
authors: BM
authors: Ure
authors: A M
authors: AM
authors: Holschneider
authors: M
authors: M
authors: Gharib
authors: H
authors: H
authors: Halsband
authors: D
authors: D
authors: Hinselmann
mesh_terms: D000008:Abdominal Neoplasms / Q000601:surgery; D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005260:Female; D005350:Fibroma / Q000145:classification / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D009364:Neoplasm Recurrence, Local / Q000601:surgery; D009378:Neoplasms, Multiple Primary / Q000145:classification / Q000601:surgery*; D011379:Prognosis; D012983:Soft Tissue Neoplasms / Q000145:classification / Q000601:surgery*
vernacular_title: Zur Klinik, Klassifikation und Prognose von 7 Fällen kindlicher Fibromatosen.