Left atrial isomerism combined with right-sided heart, common atrium, incomplete atrioventricular septal defect and partial anomalous systemic and pulmonary venous drainage. Report of a case with successful surgical correction.
Precise preoperative diagnostic clarification was accomplished in an infant with left atrial isomerism. The inner/outer arrangement of the pulmonary/systemic veins in relation to the posterior wall of the common atrium necessitated a specific baffle in order to prevent pulmonary or systemic venous obstruction. The development of a sick sinus syndrome six months after surgery is in keeping with the natural history of the disease.
Ahmadi
A
A
Department of Cardiovascular Surgery, University of Freiburg Clinics, F.R.G.
Mocellin
R
R
Spillner
G
G
D001807:Blood Vessel Prosthesis; D003914:Dextrocardia / Q000601:surgery; D005260:Female; D006325:Heart Atria / Q000002:abnormalities; D006330:Heart Defects, Congenital / Q000601:surgery*; D006344:Heart Septal Defects, Atrial / Q000601:surgery; D006345:Heart Septal Defects, Ventricular / Q000601:surgery; D006801:Humans; D007223:Infant; D010138:Pacemaker, Artificial; D011183:Postoperative Complications / Q000628:therapy; D011667:Pulmonary Veins / Q000002:abnormalities / Q000601:surgery; D012804:Sick Sinus Syndrome / Q000628:therapy; D014684:Venae Cavae / Q000002:abnormalities