title: Case report of biliary atresia associated with preduodenal portal vein, ventricular septal defect and bilobed spleen.
abstract: A case report of biliary atresia associated with preduodenal portal vein is presented with a review of 27 similar cases previously reported. The occurrence of associated anomalies in these 28 cases has a much higher frequency (82%) than coincidental association. They were associated with cardiovascular anomalies in 71%, polysplenia in 68%, malrotation of the intestine in 61%, situs inversus in 22% and duodenal atresia in 9%. Developmental anomaly is considered to participate strongly in the aetiology of biliary atresia combined with preduodenal portal vein.
authors.affiliation: Second Department of Surgery, Yamagata University School of Medicine, Japan.
authors.forename: I
authors.initials: I
authors.lastname: Yamagiwa
authors.forename: M
authors.initials: M
authors.lastname: Ohta
authors.forename: K
authors.initials: K
authors.lastname: Obata
authors.forename: M
authors.initials: M
authors.lastname: Washio
mesh_terms: D001652:Bile Ducts / Q000473:pathology; D001656:Biliary Atresia / Q000473:pathology*; D006345:Heart Septal Defects, Ventricular / Q000473:pathology*; D006346:Heart Septum / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011169:Portal Vein / Q000002:abnormalities* / Q000473:pathology; D013154:Spleen / Q000002:abnormalities* / Q000473:pathology; D013577:Syndrome