[Myocardial fibrosis in 2 children with cystic fibrosis].
We describe the cases of two patients of 9 and 15 months of age who presented episodes of congestive heart failure at the age of 9 and 10 months respectively and who were diagnosed of cystic fibrosis. Death occurred during the first year after diagnosis due to heart failure. Necroscopic study showed pancreatic affectation and heart lesions consisting in areas of myocardial fibrosis and necrosis. We discuss the different hypotheses relating pancreatic affectation to myocardial fibrosis.
Servicio de Pediatría, Unidad de Gastroenterologia, Hospital Ramón y Cajal, Madrid.
M P
MP
González
L
L
Suárez
C
C
Camarero
H
H
Escobar
D009202:Cardiomyopathies / Q000150:complications* / Q000473:pathology; D003550:Cystic Fibrosis / Q000150:complications* / Q000473:pathology; D005260:Female; D005355:Fibrosis / Q000473:pathology; D006333:Heart Failure / Q000150:complications / Q000473:pathology; D006801:Humans; D007223:Infant; D008297:Male
Fibrosis miocardia en dos niños con fibrosis quística.