[Disease picture of primary chronic intestinal pseudo-obstruction in childhood].
Primary CIPSO involves ileus symptoms without mechanical occlusion; these are caused by absence or ineffectiveness of peristalsis despite normal intestinal wall structure. The neonatal and adult types are differentiated. Ileus is progressive in the neonatal clinical pictures of CIPSO (neonatal CIPSO, MMIHS, congenital short-bowel syndrome) and chronic in the adult type, where it is also ultimately fatal, however. The problems of diagnosis and therapy are discussed and demonstrated in 5 children with primary CIPSO.
Abteilung für Kinderchirurgie, im Klinikum Steglitz Freien Universität Berlin.
R
R
Ribbe
J
J
Waldschmidt
W
W
Biewald
D000328:Adult; D005769:Gastrointestinal Motility; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D007415:Intestinal Obstruction / Q000000981:diagnostic imaging; D007418:Intestinal Pseudo-Obstruction / Q000151:congenital / Q000000981:diagnostic imaging* / Q000601:surgery; D011183:Postoperative Complications / Q000601:surgery; D011859:Radiography; D012086:Reoperation; D012778:Short Bowel Syndrome / Q000000981:diagnostic imaging
Zum Krankheitsbild der primären chronischen intestinalen Pseudoobstruktion (CIPSO) im Kindesalter.