[Divry-Van Bogaert cortico-meningeal angiomatosis and Sneddon's syndrome. Nosological study. Apropos of 4 cases].
Four patients with idiopathic livedo reticularis and multiple cerebral ischemic events leading to a severe dementia are reported. Imaging (CT, MRI, angiograms) and pathological features (in one case) are presented. Similar clinical features have been described previously in Divry-van Bogaert's disease and Sneddon's syndrome. Data from our cases and a review of the literature did not find distinctive characteristic between these entities. Thus, for practical purposes, considering them as one group appears at present warranted.
Service de Neurologie, Hôpital du Haut-Lévêque, Pessac.
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E
Ellie
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Julien
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Henry
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Vital
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Ferrer
D000328:Adult; D000798:Angiomatosis / Q000150:complications*; D002545:Brain Ischemia / Q000150:complications* / Q000473:pathology; D001932:Brain Neoplasms / Q000150:complications*; D002339:Carotid Arteries / Q000000981:diagnostic imaging; D003704:Dementia / Q000209:etiology*; D006801:Humans; D008297:Male; D008875:Middle Aged; D011859:Radiography; D012871:Skin Diseases / Q000150:complications*; D013577:Syndrome
Angiomatose cortico-méningée de Divry-Van Bogaert et syndrome de Sneddon. Etude nosologique. A propos de quatre cas.