[Divry-Van Bogaert cortico-meningeal angiomatosis and Sneddon's syndrome. Nosological study. Apropos of 4 cases].
Four patients with idiopathic livedo reticularis and multiple cerebral ischemic events leading to a severe dementia are reported. Imaging (CT, MRI, angiograms) and pathological features (in one case) are presented. Similar clinical features have been described previously in Divry-van Bogaert's disease and Sneddon's syndrome. Data from our cases and a review of the literature did not find distinctive characteristic between these entities. Thus, for practical purposes, considering them as one group appears at present warranted.
Ellie
E
E
Service de Neurologie, Hôpital du Haut-Lévêque, Pessac.
Julien
J
J
Henry
P
P
Vital
C
C
Ferrer
X
X
D000328:Adult; D000798:Angiomatosis / Q000150:complications*; D002545:Brain Ischemia / Q000150:complications* / Q000473:pathology; D001932:Brain Neoplasms / Q000150:complications*; D002339:Carotid Arteries / Q000000981:diagnostic imaging; D003704:Dementia / Q000209:etiology*; D006801:Humans; D008297:Male; D008875:Middle Aged; D011859:Radiography; D012871:Skin Diseases / Q000150:complications*; D013577:Syndrome
Angiomatose cortico-méningée de Divry-Van Bogaert et syndrome de Sneddon. Etude nosologique. A propos de quatre cas.