title: Targeting of nuclear-encoded proteins to the mitochondrial matrix: implications for human genetic defects.
authors.forename: L E
authors.initials: LE
authors.lastname: Rosenberg
authors.forename: W A
authors.initials: WA
authors.lastname: Fenton
authors.forename: A L
authors.initials: AL
authors.lastname: Horwich
authors.forename: F
authors.initials: F
authors.lastname: Kalousek
authors.forename: J P
authors.initials: JP
authors.lastname: Kraus
mesh_terms: D000595:Amino Acid Sequence; D002467:Cell Nucleus / Q000378:metabolism; D003001:Cloning, Molecular; D004734:Energy Metabolism; D004798:Enzymes / Q000235:genetics / Q000378:metabolism; D006801:Humans; D008661:Metabolism, Inborn Errors / Q000235:genetics / Q000378:metabolism*; D008928:Mitochondria / Q000378:metabolism*; D008954:Models, Biological; D009954:Ornithine Carbamoyltransferase / Q000235:genetics / Q000378:metabolism; D021382:Protein Sorting Signals / Q000235:genetics / Q000378:metabolism; D011506:Proteins / Q000235:genetics / Q000378:metabolism*
chemical_list: D004798:Enzymes; D021382:Protein Sorting Signals; D011506:Proteins; D009954:Ornithine Carbamoyltransferase