Russell-Silver syndrome: microdontia and other pertinent oral findings.
The pertinent clinical systemic and oral findings have been presented. Systemically, the patient presented with prenatal onset of growth retardation marked by an initial low birth weight, hemiatrophy, normal head size, frontal bossing, and triangular facies. Oral findings include an intact appearing primary dentition marked by microdontia, congenital absence of second premolars, blunted condyles, decreased anterior and posterior cranial base lengths, a mild hypoplastic mandible, and decreased facial height.
Cullen
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CL
Wesley
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RK
D000848:Anodontia / Q000473:pathology; D002675:Child, Preschool; D005260:Female; D005317:Fetal Growth Retardation / Q000473:pathology*; D006801:Humans; D008334:Mandible / Q000002:abnormalities*; D011247:Pregnancy; D013577:Syndrome; D014071:Tooth Abnormalities / Q000473:pathology*