Chronic eosinophilic pneumonia in a patient with ataxia telangiectasia.
The first reported case of chronic eosinophilic pneumonia in a patient with ataxia telangiectasia is described. The patient displayed the immunoglobulin deficiencies and abnormalities of lymphocyte numbers characteristic of ataxia telangiectasia. Treatment with corticosteroids led to a dramatic recovery. The proposed pathogenetic mechanisms of chronic eosinophilic pneumonia are discussed in the light of the immunological abnormalities associated with ataxia telangiectasia.
Zagami
A S
AS
Department of Neurology, Prince Henry Hospital, Little Bay, NSW.
Colebatch
H J
HJ
Wakefield
D
D
D000328:Adult; D001260:Ataxia Telangiectasia / Q000150:complications* / Q000276:immunology; D002908:Chronic Disease; D005260:Female; D006801:Humans; D007136:Immunoglobulins / Q000172:deficiency; D011241:Prednisone / Q000627:therapeutic use; D011657:Pulmonary Eosinophilia / Q000188:drug therapy / Q000209:etiology* / Q000276:immunology
D007136:Immunoglobulins; D011241:Prednisone