[Histiocytosis X: localized and disseminated forms. Apropos of 13 cases].
The authors present a study of 13 patients, between 7 months and 4 years of age diagnosed, of histiocytosis X, nine of them with a disseminated form and 4 with a localized form. The clinical and histopathologic types of presentation are analyzed, applying the usual scores of prognostic evaluation, with emphasis on the low mortality rate (one death), considering that there are several patients with bad prognostic scores. This is explained by the positive effect of chemotherapy used in these cases.
D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D001859:Bone Neoplasms / Q000473:pathology* / Q000628:therapy; D002675:Child, Preschool; D002699:Chlorambucil / Q000008:administration & dosage; D003131:Combined Modality Therapy; D005134:Eye Neoplasms / Q000473:pathology / Q000628:therapy; D005260:Female; D006646:Histiocytosis, Langerhans-Cell / Q000473:pathology* / Q000628:therapy; D006801:Humans; D007223:Infant; D008297:Male; D011241:Prednisone / Q000008:administration & dosage; D011379:Prognosis; D012878:Skin Neoplasms / Q000473:pathology / Q000628:therapy; D014747:Vinblastine / Q000008:administration & dosage; D014750:Vincristine / Q000008:administration & dosage
D002699:Chlorambucil; D014750:Vincristine; D014747:Vinblastine; D011241:Prednisone
Histiocitosis X: formas localizadas y diseminadas. A propósito de 13 casos.