title: [Sacral chordoma, a rare tumor].
abstract: One case of chordoma is described. A review of literature shows that this condition is rare. This malignant tumor grows slowly. The symptoms owing to the surrounding structures compression appear insidiously. Standard radiography, tomography, echography and computed tomography are an aid to diagnosis confirmed by biopsy. Surgical removal of the tumor is the primary modality of treatment. Surgical resection is carried out using a combined abdominal and trans-sacral approach. Complete tumoral resection is limited by preservation of sacral stability and urinary and fecal continence. Many patients are referred for radiation therapy after subtotal resection. Local recurrence is frequent. Metastasis is rare. 90 per cent of patients are dead in ten years.
mesh_terms: D002817:Chordoma / Q000175:diagnosis / Q000532:radiotherapy / Q000601:surgery*; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011300:Preoperative Care; D011879:Radiotherapy Dosage; D012447:Sacrum / Q000000981:diagnostic imaging; D013125:Spinal Neoplasms / Q000175:diagnosis / Q000532:radiotherapy / Q000601:surgery*; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography
vernacular_title: Le chordome sacré, tumeur rare.