[Papular mucinosis. Associated dermatologic and dysimmune aspects].
Papular mucinosis (PM) is an overload disease mostly made of proteoglycans, essentially cutaneous and accompanied with a monoclonal gammapathy. In addition to the cutaneous lesions, vascular and neurological manifestations may be responsible for severe complications. The gammapathy, most often benign, does not seem always correlated with the skin involvement. We report the case of a patient with mucinosis associated with a rheumatoid polyarthritis, then with a systemic necrotizing angiitis. A review of the literature has enabled us to notice the frequency with which PM is accompanied with dysimmune diseases, especially lupus.
D000293:Adolescent; D000328:Adult; D001172:Arthritis, Rheumatoid / Q000150:complications; D005260:Female; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000150:complications; D008659:Metabolic Diseases / Q000150:complications / Q000503:physiopathology; D008875:Middle Aged; D008998:Monoclonal Gammopathy of Undetermined Significance / Q000209:etiology; D009077:Mucins / Q000378:metabolism*; D012867:Skin / Q000473:pathology; D012871:Skin Diseases / Q000150:complications / Q000503:physiopathology
D009077:Mucins
Mucinose papuleuse. Aspects dermatologiques et dysimmunitaires associés.