title: Dyskinetic cilia syndrome: clinical, radiographic and scintigraphic findings.
abstract: The clinical, electron microscopic and radiographic data of 9 patients with dyskinetic cilia syndrome (DCS) are presented. Scintigraphic evaluation of mucociliary dynamics in six patients showed evidence of dyskinesia. Ventilation and perfusion studies were performed to evaluate obstructive lung disease. Retrospectively, bronchiectasis could be detected in 77% of the patients by analysis of the chest radiograph and lung scintigraphy, and bronchography potentially avoided in the seven patients who underwent this procedure.
mesh_terms: D001706:Biopsy; D001987:Bronchiectasis / Q000175:diagnosis; D001995:Bronchography; D002648:Child; D002675:Child, Preschool; D002923:Cilia / Q000473:pathology; D002925:Ciliary Motility Disorders / Q000175:diagnosis*; D005260:Female; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging; D008297:Male; D009942:Organometallic Compounds; D004369:Pentetic Acid; D011877:Radionuclide Imaging; D013668:Technetium Tc 99m Aggregated Albumin; D016284:Technetium Tc 99m Pentetate; D014980:Xenon Radioisotopes
chemical_list: D009942:Organometallic Compounds; D013668:Technetium Tc 99m Aggregated Albumin; D014980:Xenon Radioisotopes; D004369:Pentetic Acid; D016284:Technetium Tc 99m Pentetate