[The association of megaesophagus, Binder's syndrome and dysautonomia: a new neurocristopathy].
A case of esophageal achalasia is reported in a 12 year-old child. Nasal hypoplasia (Binder syndrome) and dysautonomia were associated. This may be explained by the common embryologic origin (neural crests) of nasal bud, autonomic nervous system and digestive intramural neurons. Such a neurocristopathy suggests exploration of the autonomic nervous system in cases of esophageal achalasia.
D001342:Autonomic Nervous System Diseases / Q000150:complications*; D002648:Child; D004931:Esophageal Achalasia / Q000150:complications*; D006801:Humans; D008297:Male; D009666:Nose / Q000002:abnormalities*
Association méga-oesophage, syndrome de Binder et dysautonomie: une nouvelle neurocristopathie?