Splenic lymphangiomatosis: a rare cause of splenomegaly.
A case of lymphangiomatosis of the spleen and adrenal in a 10-year-old girl is described. The patient had multiple recurrent lymphangiomata excised from her neck during the first 4 years of life. She presented with a recurrent cystic hygroma of the neck and was found to have an enlarged spleen. This increased in size during 5 months of observation, causing left upper quadrant discomfort, and was excised. The diagnosis, management, and prognosis of this rare disorder are discussed.
D000310:Adrenal Gland Neoplasms / Q000150:complications*; D002648:Child; D005260:Female; D006801:Humans; D008202:Lymphangioma / Q000150:complications*; D013160:Splenic Neoplasms / Q000150:complications*; D013163:Splenomegaly / Q000209:etiology*