title: Staged repair of supravalvular aortic stenosis associated with severe multiple peripheral pulmonary stenoses: report of extended peripheral pulmonary arterioplasty.
abstract: This paper describes surgical experience in supravalvular aortic stenosis associated with severe multiple peripheral pulmonary stenoses treated by a staged approach: initial staged repair of the bilateral pulmonary stenoses by arterioplasty through a thoracotomy and later definitive intracardiac repair of supra-valvular aortic stenosis. Our experience in two cases proved that the peripheral pulmonary arteries could be exposed up to the segmental branches by dissection from the pulmonary hilum through a lateral thoracotomy without damaging the lung parenchyma. The stenotic areas could then be repaired with either a bifurcated or trifurcated pericardial patch.
mesh_terms: D001024:Aortic Valve Stenosis / Q000601:surgery*; D001157:Arterial Occlusive Diseases / Q000601:surgery*; D002648:Child; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000601:surgery*