[Severe, refractory neonatal inflammatory syndrome as the manifestation of a systemic multivisceral and meningeal syndrome].
A neonate presented with an inflammatory syndrome with multisystemic manifestations. There was no remission until age 6 years, despite anti-inflammatory treatments. Neonatal onset and neuromeningeal manifestations identified a peculiar rare inflammatory syndrome, whose relationship with juvenile rheumatoid arthritis is discussed. In the case reported, renal, abdominal, deep lymphatic and cranial involvements were present: these have not been previously reported.
D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D007249:Inflammation / Q000150:complications / Q000151:congenital*; D008297:Male; D008581:Meningitis / Q000150:complications*; D013577:Syndrome
Syndrome inflammatoire néonatal grave, rebelle, d'expression systémique multiviscérale et méningée.