[Anatomically corrected levo-malposition of the great arteries].
The term anatomically corrected malposition of the great arteries describes a very rare form of congenital heart disease. In contrast to corrected transposition of the great arteries (atrioventricular and ventriculo-arterial discordance) there is an atrioventricular and ventriculoarterial concordance. The abnormally located arteries arise above the anatomically correct ventricles, the pulmonary trunk originates above the morphologically right ventricle, the aorta arises above the morphologically left ventricle. The abnormal relation (malposition) between the great arteries results from interposition of bilateral abnormal conal myocardium with absence of aortic valve-mitral valve fibrous continuity. In this case report an anatomically corrected laevomalposition of the great arteries associated with dextrocardia and situs solitus, ventricular septal defect and bilateral abnormal conal myocardium with subpulmonary obstruction in a young infant is presented.
D001013:Aorta, Thoracic / Q000473:pathology; D006328:Cardiac Catheterization; D003914:Dextrocardia / Q000473:pathology; D004452:Echocardiography; D005260:Female; D006325:Heart Atria / Q000473:pathology; D006345:Heart Septal Defects, Ventricular / Q000473:pathology; D006352:Heart Ventricles / Q000473:pathology; D006439:Hemodynamics; D006801:Humans; D007223:Infant; D011651:Pulmonary Artery / Q000473:pathology; D014188:Transposition of Great Vessels / Q000473:pathology*
Anatomisch korrigierte Laevo-Malposition der grossen Arterien.