Complications of vaginal atresia in association with a duplicated mullerian duct.
A mullerian duct duplication with a vaginal atresia can present as a painful abdominal mass in a female caused by a hematometrocolpos and a hemosalpinx. This set of signs and symptoms, if caused by an associated unilateral vaginal atresia, may be found in a female with normal menstrual periods, and (1) can be misdiagnosed with often tragic consequences caused by unnecessary salpingectomy, or even hysterectomy; (2) can be successfully treated by creating an adequate channel for drainage through the area of vaginal atresia; and (3) has a high association with unilateral renal agenesis. Because of this last point, recognition of either a mullerian duct duplication or unilateral renal agenesis should prompt an investigation for the other abnormality.
D000293:Adolescent; D002648:Child; D005260:Female; D006399:Hematocolpos / Q000601:surgery*; D006409:Hematometra / Q000601:surgery*; D006801:Humans; D009095:Mullerian Ducts / Q000601:surgery*; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery