Adult Turner syndrome associated with chylous ascites and vascular anomalies.
An adult female with Turner syndrome presented with severe lymphedema and chylous ascites. In addition, the patient was found to have a right-sided aortic arch and a left-sided inferior vena cava. Although lymphedema is common in infants with Turner syndrome is previously unreported. In this patient, a peritoneo-venous shunt appeared to be beneficial.
D000328:Adult; D001013:Aorta, Thoracic / Q000002:abnormalities*; D002915:Chylous Ascites / Q000150:complications* / Q000601:surgery; D005260:Female; D006801:Humans; D008209:Lymphedema / Q000150:complications / Q000601:surgery; D010536:Peritoneovenous Shunt; D014424:Turner Syndrome / Q000150:complications*; D014682:Vena Cava, Inferior / Q000002:abnormalities*