title: [Russel's syndrome. Report of a case with development of precocious puberty].
abstract: The Russel's syndrome is characterized by emaciation and hyperactivity in children and is caused by hypothalamic expansive process. This report presents the typical signs of the syndrome associated with growth hormone secretion disorders and precocious puberty pattern appearing at the age of four. The pathogenesis of the disorder is discussed and related to the hypothalamus-pituitary axis dysfunction caused by the tumor growth.
mesh_terms: D001254:Astrocytoma / Q000150:complications* / Q000628:therapy; D001932:Brain Neoplasms / Q000150:complications* / Q000628:therapy; D003131:Combined Modality Therapy; D004027:Diencephalon; D004614:Emaciation / Q000209:etiology*; D005260:Female; D006801:Humans; D007223:Infant; D009765:Obesity / Q000209:etiology; D011629:Puberty, Precocious / Q000209:etiology*; D013577:Syndrome
vernacular_title: Síndrome de russel. Apresentação de um caso com desenvolvimento de puberdade precoce.