[Extensive congenital stenosis of the bulbo-membranous urethra in a child. Apropos of a case discovered in a newborn infant].
A congenital atresia of the bulbo-membranous urethra had been reported. The atresia extended for 1.5 cm. It presented early in the neonatal period with major dilatation of the upper urinary tracts. After a preliminary urinary diversion, the surgical repair through the perineum was done at the age of 18 months. Such cases are not seen frequently. This atresia must be differentiated from posterior urethral valves type III, and from other stenoses either iatrogenic, traumatic, or inflammatory. The partial atresia is the only type compatible with life. It may be presented in two forms: annular constriction or extended stenosis. The mechanism of evolution is not very clear: it is either due to a bad resorption of the urogenital membrane or a defect in the embryogenesis of the urethral tube. Treatment differs according to the site and extent of the lesion simple dilatation, internal urethrotomy, or urethroplasty in one or several stages can be done.
D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D014525:Urethral Stricture / Q000151:congenital* / Q000601:surgery; D014547:Urinary Diversion
Sténose congénitale étendue de l'urètre bulbo-membraneux chez l'enfant. A propos d'un cas à révélation néonatale.