Endogenous catabolism as source of toxic metabolites in isovaleric acidemia.
D000592:Amino Acid Metabolism, Inborn Errors / Q000178:diet therapy*; D004044:Dietary Proteins / Q000008:administration & dosage*; D045782:Hemiterpenes; D006801:Humans; D007930:Leucine / Q000378:metabolism*; D010421:Pentanoic Acids / Q000378:metabolism*; D014631:Valerates / Q000378:metabolism*
D004044:Dietary Proteins; D045782:Hemiterpenes; D010421:Pentanoic Acids; D014631:Valerates; C008216:isovaleric acid; D007930:Leucine