[Mucha-Habermann disease. Description of a case in childhood].
The authors report a case of Mucha-Habermann disease in childhood. Mucha-Habermann disease is not a very well known, though not infrequent, disease. It is characterized by recurrent erythematous-papular-vesicular skin lesions associated with arthralgia or arthritis or large joints. Prognosis is generally favourable although an evolution towards Pityriasis Lichenoides Chronica and/or Mycosis Fungoides is possible. There are not specific laboratory findings for this form. Diagnosis is essentially based on histology showing an immunopathogenetic vasculitis. At the present time there is not a safe therapy for the disease; there are however indications for the use of Erythromycin and we followed these in our therapy with positive results.
Falcini
F
F
Dipartimento di Pediatria, Università degli Studi di Firenze, Italia.
Bartolozzi
G
G
Montanelli
F
F
Pratesi
G
G
Taccetti
G
G
Tafi
L
L
Volpi
M
M
Lotti
T
T
D001168:Arthritis / Q000150:complications; D002675:Child, Preschool; D003937:Diagnosis, Differential; D004917:Erythromycin / Q000627:therapeutic use; D006801:Humans; D008297:Male; D010146:Pain / Q000150:complications; D010267:Parapsoriasis / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D010915:Pityriasis / Q000175:diagnosis; D013577:Syndrome
D004917:Erythromycin
La malattia di Mucha-Habermann. Descrizione di un caso in età pediatrica.