Patterns of pulmonary arterial anatomy and blood supply in complex congenital heart disease with pulmonary atresia.
To identify the pattern of pulmonary anatomy and pulmonary blood supply, we analyzed the angiocardiograms of 40 patients with pulmonary atresia and complex congenital heart disease. All patients but two (95%) had confluent pulmonary arteries supplied by a patent ductus arteriosus. These two patients (5%) had nonconfluent pulmonary arteries, one with major systemic-pulmonary collateral arteries and absent patent ductus arteriosus and the other with a patent ductus arteriosus supplying the right lung and small collateral arteries supplying the left. The low incidence of pulmonary arterial abnormalities and the uniform pattern of pulmonary blood supply make the patients with pulmonary atresia and complex congenital heart disease potential candidates for palliative operation without cardiac catheterization in the neonatal period.
Marino
B
B
Department of Pediatric Cardiology and Cardiac Surgery, Bambino Gesú Hospital, Rome, Italy.
Calabró
R
R
Gagliardi
M G
MG
Bevilacqua
M
M
Ballerini
L
L
Marcelletti
C
C
D000293:Adolescent; D001158:Arteries / Q000473:pathology; D002648:Child; D002675:Child, Preschool; D002932:Cineangiography; D003097:Collateral Circulation; D004374:Ductus Arteriosus, Patent / Q000473:pathology; D006330:Heart Defects, Congenital / Q000473:pathology*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008168:Lung / Q000098:blood supply*; D011651:Pulmonary Artery / Q000002:abnormalities*; D011652:Pulmonary Circulation; D012189:Retrospective Studies