[Status epilepticus in the Lennox-Gastaut syndrome].
Thirty patients with the Lennox-Gastaut syndrome presenting one or more status epilepticus (the first before age 15) were studied. Triggering factors, semiology, duration, severity and EEG features were considered. A comparison was made between this group of patients and another group having the Lennox-Gastaut syndrome but without status. No significant difference appears in the long-term prognosis, even when status were prolonged. Only three patients died during a status. For this reason the authors recommend prudence and avoidance of very strong treatment. In their experience, intravenous diazepines, intravenous phenytoin and intramuscular ACTH were the most effective drugs.
Dravet
C
C
Natale
O
O
Magaudda
A
A
Larrieu
J L
JL
Bureau
M
M
Roger
J
J
Tassinari
C A
CA
D000293:Adolescent; D000328:Adult; D002648:Child; D004569:Electroencephalography; D005260:Female; D006801:Humans; D008297:Male; D011379:Prognosis; D012189:Retrospective Studies; D013226:Status Epilepticus / Q000150:complications / Q000188:drug therapy / Q000503:physiopathology*; D013577:Syndrome
Les états de mal dans le syndrome de Lennox-Gastaut.