Ventricular inversion and tricuspid atresia (VITA complex): long survival without surgical treatment.
Five patients with ventricular inversion, corrected transposition of the great arteries, and atresia of the left-sided atrioventricular (tricuspid) valve have been observed. Three patients died in infancy, two had large interatrial communications, one with an early stage of arterial-type hypertensive pulmonary vascular disease, and the third patient had a very small interatrial communication and severe cyanosis. The other two patients survived into adulthood; both had small interatrial communications, and one had severe venous-type hypertensive pulmonary vascular disease. The longer survival of the two patients is attributed to a balance between resistance and blood flow in the pulmonary circulation influenced by the size of the interatrial communication.
Tazelaar
H D
HD
Moore
G W
GW
Hutchins
G M
GM
D000293:Adolescent; D000328:Adult; D006328:Cardiac Catheterization; D002648:Child; D002675:Child, Preschool; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000473:pathology / Q000503:physiopathology; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011660:Pulmonary Heart Disease / Q000503:physiopathology; D014188:Transposition of Great Vessels / Q000473:pathology* / Q000503:physiopathology; D014261:Tricuspid Valve / Q000002:abnormalities*