[A rare cervical malformation syndrome: mento-sternal cleft. Apropos of 4 case reports].
Midline cervical cleft and webbing is a rare congenital anomaly of the neck. A series of 4 cases is reported, among which 2 relapses. The neonatal diagnosis of the deformation leads to a surgical treatment for the first two years, associating excision of the cleft with its underlying fibrous cord, and closure with local plasty (wave-plasty, multiple Z-plasty). However, relapses are possible. They show evidence of a real regional hypoplasia that will require the contribution of tissue. Myo cutaneous flaps are used in 3 cases. The possibility of tissue-expansion is discussed. Mandibular surgery may be necessary at a later stage (genioplasty).
Service de Stomatologie et Chirurgie Maxillo-Faciale, Centre Hospitalier Lyon Sud.
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Breton
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Dodat
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M
Freidel
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D002680:Chin / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D008297:Male; D009333:Neck / Q000002:abnormalities* / Q000601:surgery; D013249:Sternum / Q000002:abnormalities*; D013524:Surgical Flaps; D013577:Syndrome
Un syndrome malformatif cervical rare: la fissure mento-sternale. A propos de 4 observations.