Unusual cardiac manifestations in a patient with myotonic muscular dystrophy.
We report on a patient with myotonic muscular dystrophy in whom mitral valve prolapse associated with prolonged PR interval and left anterior hemiblock was documented 3 years before any clinical evidence of myotonia, muscle weakness or wasting. One year after diagnosis had been established, he developed atrial flutter with 1:1 atrioventricular conduction, an arrhythmia that in addition to complete heart block and ventricular arrhythmias may account for the occurrence of syncope and sudden death in this group of patients.
D000328:Adult; D001145:Arrhythmias, Cardiac / Q000175:diagnosis*; D004562:Electrocardiography; D004576:Electromyography; D006327:Heart Block / Q000175:diagnosis; D006801:Humans; D008297:Male; D008945:Mitral Valve Prolapse / Q000175:diagnosis*; D009136:Muscular Dystrophies / Q000175:diagnosis*