title: [Hypoattenuating lesions of the basal ganglia associated with pyramido-extrapyramidal features: report of two cases in brothers].
abstract: Two cases (siblings) with computed tomography showing slow attenuation of basal ganglia are reported. In case 1 the abnormality is larger, bilateral and the most important neurological features are: dystonic postures mainly in lower extremities and very active patellar reflexes with sustained knee clonus on both sides. In case 2 the tomographic examination disclosed a similar, but more discrete lesion only on the left side; the neurological examination is normal despite a history of frequent falls. The authors discuss the differential diagnosis from a clinical and tomographic approach.
mesh_terms: D001480:Basal Ganglia Diseases / Q000175:diagnosis / Q000235:genetics*; D001921:Brain / Q000000981:diagnostic imaging; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008297:Male; D014057:Tomography, X-Ray Computed
vernacular_title: Lesões hipoatenuantes dos gânglios da base associadas a quadro pirâmido-extrapiramidal: relato dos casos de dois irmãos.