Vaginal and phallic urethra with prominent clitoris in female pseudohermaphroditism.
Idiopathic female pseudohermaphroditism associated with a vaginal urethra, prominent clitoris and an accessory phallic urethra is a rare syndrome, with no apparent cause to account for the masculinization of the genitalia and exhibit of similar characteristic features. We report such a case and review the pertinent literature.
D002675:Child, Preschool; D002987:Clitoris / Q000002:abnormalities*; D012734:Disorders of Sex Development / Q000473:pathology*; D005260:Female; D006801:Humans; D013577:Syndrome; D014521:Urethra / Q000002:abnormalities*; D014549:Urinary Incontinence / Q000209:etiology; D014621:Vagina / Q000002:abnormalities*