Double orifice mitral valve associated with endocardial cushion defect.
Duplication of the mitral valve is a rare congenital cardiac anomaly. We encountered a case of duplication of the mitral valve associated with a partial form of endocardial cushion defect in a 6-year-old girl. The mitral orifice was separated by a fibrous tissue and each orifice provided papillary muscle and complete subvalvular mechanisms except for the cleft region. The fibrous tissue also provided a subvalvular apparatus. The cleft was repaired without complication. The short axis view of the two-dimensional echocardiogram demonstrated two separate holes in the mitral valve, which constituted the most obvious diagnostic sign prior to surgery.
D002648:Child; D004452:Echocardiography; D004694:Endocardial Cushion Defects / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D005260:Female; D006343:Heart Septal Defects / Q000150:complications*; D006801:Humans; D008943:Mitral Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D011859:Radiography