Anastomosis of systemic veins to pulmonary arteries for physiologic repair of asplenia syndrome.
In a patient with single ventricle, mitral atresia, common atrium, pulmonary stenosis, azygos continuation of the inferior vena cava and bilateral systemic artery--pulmonary artery anastomoses, the systemic veins were connected directly to the pulmonary arteries to achieve physiologic repair; the child was discharged five days after surgery and is asymptomatic three years postoperatively. This case illustrates the usefulness of azygos continuation of the inferior vena cava and emphasizes the need for low pulmonary artery pressure when a cavopulmonary anastomosis is done.
D000792:Angiography; D001166:Arteriovenous Shunt, Surgical; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D011651:Pulmonary Artery / Q000601:surgery*; D013154:Spleen / Q000002:abnormalities*; D013577:Syndrome; D014680:Veins / Q000601:surgery*; D014682:Vena Cava, Inferior / Q000002:abnormalities*