title: [Regional hypoplasia of dermal lymphatic vessels--a new variant of congenital lymphedema].
abstract: The value of new investigative methods of the most peripheral lymphatics of the skin (fluorescence microlymphography, indirect lymphography) is demonstrated by the case report of an 18 year-old girl. Regional hypoplasia of dermal lymphatics was detected in the lymphoedematous proximal and middle phalanges of the fingers while the initial lymphatics of the normal-appearing distal phalanges showed no obvious change. The subcutaneous lymph-collectors were ectatic and increased in the oedematous parts as well as in the normal-looking ends of the fingers. Hence, this is a new variant of lymphoedema, which is not caused by hypoplasia of lymph-collectors, but by a regional lack of initial lymphatics of the skin.
mesh_terms: D000293:Adolescent; D005260:Female; D005385:Fingers / Q000000981:diagnostic imaging; D006225:Hand / Q000000981:diagnostic imaging; D006801:Humans; D008208:Lymphatic System / Q000002:abnormalities*; D008209:Lymphedema / Q000151:congenital* / Q000000981:diagnostic imaging; D008220:Lymphography; D012868:Skin Abnormalities
vernacular_title: Regionale Hypoplasie dermaler Lymphgefässe--eine neue Variante des kongenitalen Lymphödems.