Familial pheochromocytoma in a child with multiple recurrence including a lesion in the intrathoracic region.
Familial pheochromocytomas were removed from the bilateral adrenal glands and the abdominal cavity of a 10-year-old female. Due to the existence of an accessory adrenal gland, it was possible to discontinue steroid supplement. The disease relapsed, however, when she was 15 years old. After removing the ectopic pheochromocytomas from the abdominal cavity and thorax, she was free from symptoms for 2 years and 6 months.
D000310:Adrenal Gland Neoplasms / Q000235:genetics*; D002648:Child; D005260:Female; D006801:Humans; D008479:Mediastinal Neoplasms / Q000235:genetics; D008638:Mesenteric Arteries; D009364:Neoplasm Recurrence, Local; D010673:Pheochromocytoma / Q000235:genetics*; D012445:Sacrococcygeal Region