[Pulmonary artery loop and dysplastic tracheal stenosis. Case report with pre- and postoperative spirometry and discussion of the value of diagnostic signs].
Since his second week of life a boy, with pulmonary artery sling now 8 3/4 years old suffered from mainly expiratory stridor during exercise and dyspnoe during bronchopulmonary infections, twice in a life-threatening manner. The indirect diagnostic signs were all negative, bronchoscopy revealed a narrow distal trachea and a pulsating stenosis of high degree at the bifurcation. Bronchographic findings were characteristic. Angiocardiographically the retrotracheal run of the left pulmonary artery could only be proved by marking the trachea with a catheter. After operation at the age of 8 1/4 years, the boy had no relevant subjective complaints during a follow-up of 6 months. Spirometric lung function tests before and after corrective operation revealed a considerable obstruction of central intrathoracic airways that persisted after operation, only peak flow improved significantly. According to the bronchological findings the reason therefore is a dysplastic tracheobronchial stenosis, which is seen often in combination with PAS.
D001995:Bronchography; D006328:Cardiac Catheterization; D002648:Child; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities*; D014135:Tracheal Stenosis / Q000151:congenital* / Q000175:diagnosis
Pulmonalarterienschlinge und dysplastische Trachealstenose. Fallbericht mit prä- und postoperativer Spirometrie und Diskussion der Wertigkeit der diagnostischen Zeichen.