A case of biliary atresia and polysplenia. Evaluation by hepatobiliary scintigraphy.
A 5-week old jaundiced female underwent hepatobiliary scintigraphy using technetium-99m disofenin. Early images suggested right-sided cardiac activity. A nearly symmetric, bilobed liver with left-sided predominance was discovered. No biliary ducts, gallbladder, or small bowel activity were demonstrated up to 24 hours post-injection. Laparotomy confirmed situs inversus, polysplenia, and extrahepatic biliary atresia.
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D001656:Biliary Atresia / Q000000981:diagnostic imaging*; D001659:Biliary Tract / Q000000981:diagnostic imaging; D002828:Choristoma / Q000000981:diagnostic imaging*; D005260:Female; D005704:Gallbladder / Q000002:abnormalities / Q000000981:diagnostic imaging; D006801:Humans; D007098:Imino Acids; D007223:Infant; D008099:Liver / Q000000981:diagnostic imaging; D009942:Organometallic Compounds; D011877:Radionuclide Imaging; D012857:Situs Inversus / Q000000981:diagnostic imaging; D013154:Spleen; D013667:Technetium; D019785:Technetium Tc 99m Disofenin
D007098:Imino Acids; D009942:Organometallic Compounds; D013667:Technetium; D019785:Technetium Tc 99m Disofenin