Massive bleeding in neurofibromatosis associated with congenital hypofibrinogenaemia: a case report.
A 22 year old male who bled profusely at operation for excision of an extensive scalp and facial neurofibromata is reported. He was found to have congenital hypofibrinogenaemia. It is suggested that hypofibrinogenaemia should be considered as a cause of excessive bleeding in cases of Von Recklinghausen's neurofibromatosis.
D000328:Adult; D000347:Afibrinogenemia / Q000150:complications / Q000151:congenital*; D006258:Head and Neck Neoplasms / Q000150:complications* / Q000601:surgery; D006470:Hemorrhage / Q000209:etiology*; D006801:Humans; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000151:congenital / Q000601:surgery; D010375:Pedigree