Diffuse neonatal hemangiomatosis.
Diffuse neonatal hemangiomatosis is an often fatal disorder characterized by widespread capillary hemangiomas of the skin and visceral organs. Ultrasound and computed tomographic scans may be useful in determining the extent of visceral disease. The organs most commonly affected are the gastrointestinal tract, brain, liver, and lung. Complications include high-output cardiac failure, gastrointestinal bleeding, hydrocephalus, and consumption coagulopathy. Despite therapy with corticosteroids, the mortality rate is high.
D001932:Brain Neoplasms / Q000473:pathology; D005153:Facial Neoplasms / Q000473:pathology; D005260:Female; D006391:Hemangioma / Q000097:blood / Q000151:congenital* / Q000188:drug therapy; D006801:Humans; D007231:Infant, Newborn; D008113:Liver Neoplasms / Q000473:pathology; D008775:Methylprednisolone / Q000627:therapeutic use; D009062:Mouth Neoplasms / Q000473:pathology; D009378:Neoplasms, Multiple Primary / Q000151:congenital*; D012878:Skin Neoplasms / Q000151:congenital*
D008775:Methylprednisolone