Cutaneous segmental neurofibromatosis.
Two patients with multiple cutaneous neurofibromas restricted to a dermatomal portion of the skin are described. Neither patient had clinical evidence or a family history of generalized neurofibromatosis. Whether this represents a distinct disorder, sui generis, or a variant in the spectrum of neurofibromatosis is unknown.
D000293:Adolescent; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000235:genetics / Q000473:pathology*; D012867:Skin / Q000473:pathology*; D012878:Skin Neoplasms / Q000235:genetics / Q000473:pathology*