title: [Ganglioneuroblastoma of the orbit].
abstract: Ganglioneuroblastoma a transitional tumor of sympathetic origin has not yet been described as involving orbit. It is characterized by a mixture of cells ranging from primitive neuroblast to well differentiated ganglion cells within a neurofibromatous tissue. The prognosis is uncertain, as the tumor may either undergo maturation into a ganglioneuroma or may metastasize widely and rapidly as in neuroblastoma. We may postulate a relationship between ganglioneuroblastoma and Recklinghausen's neurofibromatosis in view of the development of the tumor in conjunction with the phacomatosis.
mesh_terms: D002471:Cell Transformation, Neoplastic / Q000473:pathology; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005729:Ganglioneuroma / Q000473:pathology* / Q000503:physiopathology / Q000628:therapy; D006801:Humans; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D009447:Neuroblastoma / Q000473:pathology / Q000503:physiopathology; D009456:Neurofibromatosis 1 / Q000473:pathology; D009918:Orbital Neoplasms / Q000473:pathology* / Q000628:therapy; D011379:Prognosis; D012878:Skin Neoplasms / Q000473:pathology
vernacular_title: Ganglioneuroblastome de l'orbite.