Congenital complete heart block with maternal primary Sjögren's syndrome.
We have described a case of congenital complete heart block associated with maternal primary Sjögren's syndrome. This diagnosis should also be considered when evaluating mothers of children with congenital heart block, especially when no connective tissue disease is otherwise clinically apparent. The potential significance of antibodies to SSA in this association remains to be determined.
D002311:Cardiomyopathy, Dilated / Q000151:congenital; D004695:Endocardial Fibroelastosis / Q000151:congenital; D005260:Female; D006327:Heart Block / Q000151:congenital*; D006801:Humans; D007231:Infant, Newborn; D008046:Lip / Q000473:pathology; D008297:Male; D012859:Sjogren's Syndrome / Q000473:pathology*