Pancreoblastoma in a neonate associated with Beckwith-Wiedemann syndrome.
A cystic abdominal mass was removed from a male child born at 32 weeks gestation. Histological examination showed this to be a pancreoblastoma. Both clinical and histological features of Beckwith-Wiedemann syndrome developed within the first 12 weeks of life. The child remains well and thriving with no tumour recurrence at 10 months of age.
D001506:Beckwith-Wiedemann Syndrome / Q000473:pathology*; D004848:Epithelium / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D008854:Microscopy, Electron; D010179:Pancreas / Q000473:pathology; D010181:Pancreatic Cyst / Q000473:pathology* / Q000601:surgery; D010190:Pancreatic Neoplasms / Q000473:pathology* / Q000601:surgery; D011183:Postoperative Complications / Q000473:pathology