The knee in arthrogryposis.
Of 104 patients with arthrogryposis multiplex congenita treated between 1952 and 1982, 74 had significant knee contractures, instability, or recurvatum. The minimum follow-up period was two years. Nonoperative treatment modalities included physical therapy, bracing, and serial casting in 43 patients (78 knees). Thirty-one other patients (46 knees) had 62 operative procedures, including hamstring and posterior capsular release, epiphysiodesis, distal femoral or proximal tibial osteotomy, arthrodesis, and knee disarticulation. Surgery was reserved for the more resistant causes and was recommended only as part of an overall treatment plan including the correction of foot and hip deformities. The average follow-up period for the surgically treated patients was 11 years, with a range of two to 20 years. Recurrence of deformity was frequent, with no one procedure being clearly favored. Physiotherapy alone rarely resulted in clinically significant improvement unless accompanied by prolonged casting and bracing. The most useful surgical procedure in the growing child was posterior capsular release performed in conjunction with hamstring tenotomy. Contractures treated by osteotomies before the completion of growth had a high rate of recurrence.
D001174:Arthrodesis; D001176:Arthrogryposis / Q000628:therapy*; D001915:Braces; D002370:Casts, Surgical; D002675:Child, Preschool; D004188:Disarticulation; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D007719:Knee Joint / Q000601:surgery; D008297:Male; D010027:Osteotomy; D026741:Physical Therapy Modalities; D012008:Recurrence; D013997:Time Factors