Bilateral papillary cystadenoma of the epididymis as a component of von Hippel-Lindau's syndrome: report of a case presenting as infertility.
We report a case of bilateral papillary cystadenoma of the epididymis thought to be a component of the von Hippel-Lindau syndrome. The patient was hospitalized initially because of infertility. He had undergone a craniotomy 2 years previously for the diagnosis of a cerebellar hemangioblastoma. Funduscopy had revealed angiomatous lesions of the left eye. The von Hippel-Lindau syndrome is discussed briefly and the importance of long-term urological followup for possible presentation of silent renal carcinoma is emphasized. Patients with bilateral epididymal papillary cystadenoma are prone to have other components of the von Hippel-Lindau syndrome, and clinical studies are indicated in all such patients.
D000328:Adult; D000798:Angiomatosis / Q000150:complications*; D003537:Cystadenoma / Q000150:complications* / Q000473:pathology; D004822:Epididymis; D006801:Humans; D007248:Infertility, Male / Q000209:etiology*; D008297:Male; D013736:Testicular Neoplasms / Q000150:complications* / Q000473:pathology; D006623:von Hippel-Lindau Disease / Q000150:complications* / Q000473:pathology