Cerebrovascular occlusive disease with and without the moyamoya vascular network in children.
Clinical features of cerebrovascular occlusive disease with the moyamoya network (group 1: twenty-nine children) and those without this network (group 2: nine children) are reported herein. Group 1 was characterized by female preponderance, recurrent and transient ischemic attacks, progression of mental deterioration, rebuild-up after hyperventilation on EEG and wide-spread lesions on CT scan. Group 2 had one or two attacks which led to a rather long-lasting hemiplegia but not to mental deterioration, rare rebuild-up findings on EEG and unilateral focal lesion on CT scan. Precipitating factors for ischemic attacks included deep breathing, changes in body temperature or sleep-waking transition were present in both groups. Etiology in some children was considered to be congenital.
D001157:Arterial Occlusive Diseases / Q000175:diagnosis*; D002340:Carotid Artery Diseases / Q000175:diagnosis; D002343:Carotid Artery, Internal; D002533:Cerebral Angiography; D002536:Cerebral Arteries; D002561:Cerebrovascular Disorders / Q000175:diagnosis*; D002648:Child; D003937:Diagnosis, Differential; D004569:Electroencephalography; D005260:Female; D006801:Humans; D008297:Male; D009072:Moyamoya Disease / Q000175:diagnosis*; D014057:Tomography, X-Ray Computed