Fibromuscular dysplasia of cervico-cephalic arteries with multiple dissections and a carotid-cavernous fistula. A pathological study.
A rare case of widespread fibromuscular dysplasia (F.M.D.) is reported, involving the cervico-cephalic arteries associated with multiple dissections, saccular aneurysms and a carotid-cavernous fistula. A detailed post-mortem examination revealed FMD involvement of the intracranial vessels, not demonstrated by arteriography.
D000328:Adult; D000784:Aortic Dissection / Q000473:pathology; D001011:Aorta / Q000473:pathology; D001157:Arterial Occlusive Diseases / Q000473:pathology*; D001164:Arteriovenous Fistula / Q000473:pathology*; D002339:Carotid Arteries / Q000473:pathology; D002340:Carotid Artery Diseases / Q000473:pathology*; D002426:Cavernous Sinus / Q000473:pathology*; D002539:Cerebral Arterial Diseases / Q000473:pathology*; D005260:Female; D005352:Fibromuscular Dysplasia / Q000473:pathology*; D006801:Humans; D002532:Intracranial Aneurysm / Q000473:pathology; D009333:Neck / Q000098:blood supply*