Fatal splenic rupture in Ehlers-Danlos syndrome.
A fatal case of Ehlers-Danlos syndrome (Type IV) is described. Autopsy revealed splenic rupture that had resulted from spontaneous haemorrhage into the splenic parenchyma. This is a previously unrecorded complication of Ehlers-Danlos syndrome and should be considered in the differential diagnosis of chest and abdominal pain in patients with this condition.
D000328:Adult; D003645:Death, Sudden / Q000209:etiology*; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D006801:Humans; D008297:Male; D012422:Rupture, Spontaneous; D013161:Splenic Rupture / Q000150:complications*