Atrioventricular septal defect with balanced ventricles and malaligned atrial septum: double-outlet right atrium. Report of two cases.
An unusual form of atrioventricular septal defect was found at operation. The anatomy was that of a primum atrial septal defect with deviation of the atrial septum to the left. Thus from the right atrium both right and left atrioventricular valves could be seen. The left-sided valve was tricuspid. Repair was achieved by closure of the septal commissure of the left-sided valve ("cleft"), excision of the lower part of the atrial septum, and insertion of a pericardial patch. The lower part of the patch was sutured between the left and right atrioventricular valves. A specimen with similar anatomy is also described.
D002675:Child, Preschool; D004452:Echocardiography; D004694:Endocardial Cushion Defects / Q000175:diagnosis / Q000601:surgery*; D005260:Female; D006325:Heart Atria / Q000601:surgery; D006343:Heart Septal Defects / Q000601:surgery*; D006346:Heart Septum / Q000601:surgery; D006801:Humans