Defective [U-14 C] palmitic acid oxidation in Duchenne muscular dystrophy.
Compared with normal skeletal muscle, muscle from patients with Duchenne dystrophy had decreased [U-14 C] palmitic acid oxidation. [1-14 C] palmitic acid oxidation was normal. These results may indicate a defect in intramitochondrial fatty acid oxidation.
D000293:Adolescent; D000328:Adult; D002250:Carbon Radioisotopes; D002648:Child; D002675:Child, Preschool; D006801:Humans; D007223:Infant; D009136:Muscular Dystrophies / Q000378:metabolism*; D010168:Palmitates / Q000378:metabolism*; D010169:Palmitic Acids / Q000378:metabolism*
D002250:Carbon Radioisotopes; D010168:Palmitates; D010169:Palmitic Acids