Brainstem auditory-evoked responses and clinical picture in a one year follow-up of 18 patients with Friedreich ataxia.
Brainstem auditory-evoked responses (BAER) and behavior audiometry were evaluated on 18 patients with Friedreich ataxia. Behavior audiometry showed a normal pure tone test, normal performance intensity and phonetically balanced functions in all patients. BAER were abnormal in all patients. The data obtained show a good correlation between BAER and clinical picture and suggest that BAER could be useful in monitoring the clinical condition of FA patients.
D000293:Adolescent; D000328:Adult; D001301:Audiometry, Pure-Tone; D001307:Auditory Perception; D001933:Brain Stem; D002648:Child; D005072:Evoked Potentials, Auditory; D005260:Female; D005621:Friedreich Ataxia / Q000503:physiopathology*; D006801:Humans; D008297:Male