Amino acid and protein requirements in a preterm infant with classic phenylketonuria.
A preterm infant with classic phenylketonuria required rather less than 90 mg/kg of phenylalanine and between 270 and 290 mg/kg tyrosine daily to achieve a rate of weight gain of around 20 g/kg per day. Using Lofenalac as the low phenylalanine food, the intake of tyrosine, an essential amino acid for patients with phenylketonuria seemed to be limiting in respect of growth.
D000596:Amino Acids / Q000008:administration & dosage*; D001835:Body Weight; D004044:Dietary Proteins / Q000008:administration & dosage*; D005260:Female; D006801:Humans; D007227:Infant Nutritional Physiological Phenomena; D007231:Infant, Newborn; D007234:Infant, Premature; D009751:Nutritional Requirements; D010649:Phenylalanine / Q000008:administration & dosage; D010661:Phenylketonurias / Q000178:diet therapy*; D014443:Tyrosine / Q000008:administration & dosage
D000596:Amino Acids; D004044:Dietary Proteins; D014443:Tyrosine; D010649:Phenylalanine