[Weber-Christian disease with systemic involvement. Apropos of a case of histiocytic cytophagous panniculitis].
A case of systemic Weber-Christian disease involving the liver and medulla, with pancytopenia and disseminated intravascular coagulation (DIC) is reported. Clinical and histopathological diagnostic criteria are stressed. Post-mortem findings are described.
D001853:Bone Marrow / Q000473:pathology; D004211:Disseminated Intravascular Coagulation / Q000473:pathology*; D005260:Female; D006644:Histiocytes / Q000473:pathology; D006801:Humans; D008099:Liver / Q000473:pathology; D008875:Middle Aged; D010198:Pancytopenia / Q000473:pathology; D010201:Panniculitis, Nodular Nonsuppurative / Q000097:blood / Q000473:pathology*; D010586:Phagocytes / Q000473:pathology
La malattia di Weber-Christian ad interessamento sistemico. A proposito di un caso di pannicolite istiocitica-citofagica.