[Association of Ewing's sarcoma with fibrous dysplasia of the tibia. Apropos of a case report].
The authors have observed a child of 14 presenting fibrous dysplasia localised to the right femur and right tibia and complicated by an Ewing's sarcoma of the right tibia. The complication was marked only by pain and the radiographs were not typical. It was diagnosed only by microscopic examination after biopsy. Scintigraphy did not reveal any other site of fibrous dysplasia. The tibia was treated by a reinforcing nail followed by radiotherapy and chemotherapy. After a 4 year follow-up there was neither recurrence nor metastasis. After a review of the literature it is concluded that this combination was purely accidental and that there is no known relationship between Ewing's sarcoma and Jaffe-Lichtenstein type of fibrous dysplasia. It is remarkable that the sarcoma was not typical clinically and that the satisfactory result was probably related to very early treatment.
D000293:Adolescent; D001859:Bone Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000150:complications* / Q000473:pathology; D006801:Humans; D011859:Radiography; D012512:Sarcoma, Ewing / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D013977:Tibia
Association sarcome d'Ewing et dysplasie fibreuse du tibia. A propos d'une observation.