[Early auditory evoked potentials in spinocerebellar heredodegenerative involvement].
Results of early auditory evoked potentials, recorded during exploration of spinocerebellar heredodegenerative lesions (21 cases of Friedreich's disease, 8 cases of Pierre-Marie's disease and 3 cases of Strumpell-Lorraine disease), are analyzed. Tracings showed alteration of auditory BER whereas tonal audiometry was normal. Analysis of BER demonstrated lengthening of the latency periods, a rise in thresholds without latency period increases and a tracing that was sometimes flat or with waves that were difficult to recognize.
D000293:Adolescent; D000328:Adult; D002524:Cerebellar Ataxia / Q000503:physiopathology; D002526:Cerebellar Diseases / Q000503:physiopathology*; D002648:Child; D005072:Evoked Potentials, Auditory; D005260:Female; D005621:Friedreich Ataxia / Q000503:physiopathology; D006801:Humans; D008297:Male; D009128:Muscle Spasticity / Q000235:genetics; D010264:Paraplegia / Q000235:genetics; D013997:Time Factors
Apport du potentiel évoqué auditif précoce dans les atteintes hérédo-dégénératives spino-cérébelleuses.