[Congenital hepatic fibrosis disclosed late by hepatic encephalopathy].
A case of hepatic encephalopathy revealing congenital hepatic fibrosis in a 47-year-old woman is reported. The characteristic features of this observation were: a) the long clinical latency of a congenital disease usually discovered in childhood or in adolescence; b) the existence of hepatocellular insufficiency which appeared without any other reason than an ordinary infection; c) the absence of digestive bleeding or portacaval shunt, factors always found in the rare, previously described cases of encephalopathy in congenital hepatic fibrosis.
D000641:Ammonia / Q000097:blood; D003221:Confusion / Q000209:etiology; D005260:Female; D006501:Hepatic Encephalopathy / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D008099:Liver / Q000473:pathology; D008107:Liver Diseases / Q000151:congenital* / Q000175:diagnosis; D008875:Middle Aged; D013997:Time Factors
D000641:Ammonia
Fibrose hépatique congénitale tardivement révélée par une encéphalopathie hépatique.