[Short-latency brain stem evoked potentials to acoustic stimulation in patients with hereditary neuromuscular diseases].
Short-latent evoked potentials (SLEP) of the brain stem following acoustic stimulation (AS) were studied in 70 patients with hereditary neuromuscular diseases. The degree of changes in the components of brain stem SLEP in response to AS was found to correlate with disorders of impulse sensor conduction along the peripheral nerves in patients with the Roussy-Levy areflex distasia, the Charcot-Marie neural amyotrophy and Friedreich's spinocerebral ataxia. This method of recording brain stem SLEP following AS is a new modern highly informative tool of investigation allowing the physicians to assess the state of different portions of the brain stem in health and disease.
D000293:Adolescent; D000328:Adult; D001933:Brain Stem / Q000503:physiopathology*; D004594:Electrophysiology; D005072:Evoked Potentials, Auditory; D005621:Friedreich Ataxia / Q000503:physiopathology; D006801:Humans; D008875:Middle Aged; D009132:Muscles / Q000503:physiopathology; D009136:Muscular Dystrophies / Q000503:physiopathology; D009468:Neuromuscular Diseases / Q000235:genetics / Q000503:physiopathology*; D010525:Peripheral Nerves / Q000503:physiopathology; D011930:Reaction Time / Q000502:physiology; D013577:Syndrome
Korotkolatentnye stvolovye vyzvannye potentsialy na akusticheskuiu stimuliatsiiu u bol'nykh s nasledstvennymi nervno-myshechnymi zabolevaniiami.