Residual high-frequency hearing in a patient with Mondini's deformity: clinical implications.
We reviewed records of a patient with Mondini's deformity who had hearing loss in the speech frequencies and preservation of hearing for frequencies above 4000 Hz. The patient seemed to be an example of a profoundly deaf child with good speech development secondary to preservation of ultra-audiometric hearing. We suggest that patients with Mondini's deformity have their ultra-audiometric hearing evaluated, and that those with profound deafness and ultra-audiometric hearing be radiographically evaluated to rule out Mondini's deformity for diagnostic and therapeutic purposes.
D001309:Auditory Threshold; D003051:Cochlea / Q000002:abnormalities*; D005260:Female; D006311:Hearing Disorders / Q000151:congenital* / Q000503:physiopathology; D006320:Hearing Tests; D006801:Humans; D007223:Infant; D008297:Male; D008875:Middle Aged