title: Congenital cholesteatoma of the petrous pyramid.
abstract: A 20-year follow-up was done on a patient with a large congenital cholesteatoma of the petrous apex. The patient was treated successfully with marsupialization through a radical mastoidectomy and sphenoid sinusotomy. Cranial computed tomography and magnetic resonance imaging demonstrated continued cholesteatoma growth. Bone-conduction thresholds remained normal despite replacement of the internal auditory canal by cholesteatoma matrix. The patient continues to have chronic otorrhea, but is otherwise asymptomatic.
mesh_terms: D000293:Adolescent; D001847:Bone Diseases / Q000151:congenital / Q000601:surgery; D002781:Cholesteatoma / Q000151:congenital* / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D008297:Male; D008416:Mastoid / Q000601:surgery; D010579:Petrous Bone / Q000000981:diagnostic imaging / Q000601:surgery; D013101:Sphenoid Sinus / Q000601:surgery; D014057:Tomography, X-Ray Computed