New fluorometric assay of lysosomal acid lipase and its application to the diagnosis of Wolman and cholesteryl ester storage diseases.
D002784:Cholesterol / Q000031:analogs & derivatives; D002788:Cholesterol Esters / Q000378:metabolism; D006801:Humans; D008049:Lipase / Q000032:analysis* / Q000172:deficiency; D008052:Lipid Metabolism, Inborn Errors / Q000175:diagnosis* / Q000201:enzymology; D008247:Lysosomes / Q000201:enzymology*; D013050:Spectrometry, Fluorescence / Q000379:methods; D014280:Triglycerides; D014973:Xanthomatosis / Q000175:diagnosis / Q000201:enzymology
D002788:Cholesterol Esters; D014280:Triglycerides; C046440:3-(10-pyrenedecanoyl)cholesterol; C046439:1-(10-pyrenedecanoyl)-2,3-dioleoylglycerol; D002784:Cholesterol; D008049:Lipase