[Pseudo precocious puberty in the McCune-Albright syndrome].
McCune Albright Syndrome is characterized by the triad of polyostostic fibrous dysplasia of bones, skin pigmentation (café au lait-spots) and sexual precocity. The authors report a case of a 7 years girl with this syndrome in whom the sexual precocity is due to an autonomous hyperfunctioning of luteinized follicular cysts of ovary. The pathogenic mechanisms of this autonomy are debate.
D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000150:complications*; D005359:Fibrous Dysplasia, Polyostotic / Q000150:complications*; D006801:Humans; D010048:Ovarian Cysts / Q000150:complications* / Q000503:physiopathology; D011629:Puberty, Precocious / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology
Pseudo-puberté précoce dans le syndrome de McCune-Albright.