title: [Extraoral manifestation of a white sponge nevus of the mucosa].
abstract: The nevus spongiosus albus mucosae (resp. white sponge nevus in the angloamerican literature) is a hereditary leukokeratosis localised preferably in the oral mucosa, but may simultaneously manifest itself in other regions, e.g. perianally. We report the case of a 18-year old patient with a primarily and exclusively extraorally located nevus spongiosus albus mucosae of the vulva. The differential diagnosis and clinical as well as therapeutical problems of this extremely rare disease are discussed.
mesh_terms: D000293:Adolescent; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007971:Leukoplakia / Q000175:diagnosis; D013684:Telangiectasis / Q000175:diagnosis* / Q000473:pathology; D014845:Vulvar Diseases / Q000175:diagnosis* / Q000473:pathology
vernacular_title: Extraorale Manifestation eines Naevus spongiosus albus mucosae.