[Bobble-head doll syndrome].
A new case of Bobble-head doll syndrome with aqueductal stenosis is presented in a 14 year-old boy. Ventriculocisternostomy performed 8 years after the onset of the abnormal movement resulted in moderate reduction of the head bobbling. Twenty-two cases were found in a review of the literature. In all cases there was a chronic slowly progressive hydrocephalus with usually a cyst of the third ventricle; aqueductal stenosis was less frequent. When recorded, psychomotor development was impaired. Treatment is neurosurgical. Pathogenesis remains unknown.
D000293:Adolescent; D001927:Brain Diseases / Q000150:complications; D002535:Cerebral Aqueduct; D006257:Head; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology*; D008297:Male; D009069:Movement Disorders / Q000209:etiology
Syndrome de la poupée à tête ballotante. "Bobble-head doll syndrome".