Tibia vara caused by focal fibrocartilaginous dysplasia. Three case reports.
We present three cases of a previously undescribed condition characterised by unilateral tibia vara associated with an area of focal fibrocartilaginous dysplasia in the medial aspect of the proximal tibia. The three children affected were aged 9, 15 and 27 months respectively. Two required tibial osteotomy, but in one the deformity resolved without treatment. The pathogenesis of the focal lesion remains conjectural; the most likely explanation is that the mesenchymal anlage of the tibial metaphysis has, for unknown reasons, developed abnormally at the insertion of the pes anserinus.
D002357:Cartilage Diseases / Q000000981:diagnostic imaging* / Q000473:pathology; D002675:Child, Preschool; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000000981:diagnostic imaging*; D005358:Fibrous Dysplasia, Monostotic / Q000000981:diagnostic imaging* / Q000473:pathology; D006801:Humans; D007223:Infant; D008297:Male; D011859:Radiography; D013577:Syndrome; D013977:Tibia / Q000000981:diagnostic imaging* / Q000473:pathology