Univentricular heart in adults: report of nine cases with review of the literature.
Nine patients with univentricular heart 17 years of age or older were followed up for a mean duration of 13 years (range 5 to 26 years). Five patients had type A and four patients had type C univentricular heart. Pulmonary stenosis was present in eight of nine patients. Palliative shunt surgery was performed in seven patients, ventricular septation was performed in one patient, and no surgical intervention was performed in one patient. Eight patients were in New York Heart Association functional class II and one patient was in New York Heart Association functional class III. Long term follow-up of these patients suggests that a selected group of adults with univentricular heart may achieve a relatively long survival and good functional class with conservative management.
D000293:Adolescent; D000328:Adult; D005260:Female; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000473:pathology* / Q000601:surgery; D006352:Heart Ventricles / Q000473:pathology; D006439:Hemodynamics; D006801:Humans; D008297:Male