Chondrosarcoma in Maffucci's syndrome.
Nine patients with Maffucci's syndrome were seen at our institution; chondrosarcoma developed in five. On the basis of the cases of these patients and those reported in the English literature since 1973, we determined that the incidence of chondrosarcoma in patients with Maffucci's syndrome is 17.8 per cent.
D000293:Adolescent; D000328:Adult; D002356:Cartilage / Q000473:pathology; D002648:Child; D002675:Child, Preschool; D002813:Chondrosarcoma / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D004687:Enchondromatosis / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006391:Hemangioma / Q000150:complications; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D008875:Middle Aged; D010009:Osteochondrodysplasias / Q000150:complications*; D011859:Radiography