Pulmonary capillary hemangiomatosis.
We report a case of pulmonary capillary hemangiomatosis affecting a 35-yr-old Caucasian woman. Progressive pulmonary hypertension was documented by serial cardiac catheterizations, and pulmonary function studies showed changes suggestive of chronic pulmonary congestion. Although a difficult condition to diagnose during life as it may mimic veno-occlusive disease, capillary hemangiomatosis has a distinct histopathologic picture.
D000328:Adult; D000792:Angiography; D002196:Capillaries / Q000473:pathology; D005260:Female; D006391:Hemangioma / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D006801:Humans; D006976:Hypertension, Pulmonary / Q000000981:diagnostic imaging / Q000209:etiology* / Q000473:pathology; D009369:Neoplasms; D011652:Pulmonary Circulation; D013902:Radiography, Thoracic; D012129:Respiratory Function Tests; D014652:Vascular Diseases / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology