[Rare diseases of the ear: fibrous dysplasia of the tympanic bone, extensive papillomatosis, ceruminoma, aspergilloma, spontaneous évidement of the tympanic bone].
The authors report six cases of rare ear diseases: fibrous dysplasia of the tympanum mimicking an partially obstructive osteoma of the external auditory canal. The authors draw a parallel between the rarity of these monostotic forms of the temporal bone which are strictly localised to a single region (tympanum-mastoid-atrium) and the diffuse forms which involve several regions at the same time; extensive papillomatosis of the external and middle ear, a rare condition with serious repercussions; two ceruminomas with very different clinical presentations and outcomes; an atrial pseudo-tumoral aspergilloma which was easily excised ans repaired with a myringoplasty with a good long term result; hypoplasia of the tympanum, which constituted a spontaneous évidement, discovered at operation for an attic cholesteatoma. This finding was sufficiently unusual to warrant reporting.
D000230:Adenocarcinoma / Q000175:diagnosis; D000236:Adenoma / Q000175:diagnosis; D000328:Adult; D000368:Aged; D001228:Aspergillosis / Q000175:diagnosis*; D001848:Bone Diseases, Developmental / Q000175:diagnosis; D002571:Cerumen; D003937:Diagnosis, Differential; D004424:Ear Canal / Q000473:pathology; D004427:Ear Diseases / Q000175:diagnosis* / Q000628:therapy; D004428:Ear Neoplasms / Q000175:diagnosis*; D004432:Ear, Middle / Q000473:pathology; D005357:Fibrous Dysplasia of Bone / Q000175:diagnosis*; D005358:Fibrous Dysplasia, Monostotic / Q000175:diagnosis*; D006801:Humans; D008297:Male; D008875:Middle Aged; D010016:Osteoma / Q000175:diagnosis; D010212:Papilloma / Q000175:diagnosis*; D013701:Temporal Bone / Q000473:pathology*
Quelques affections rares de l'oreille: dysplasie fibreuse du tympanal, papillomatose extensive, céruminome, aspergillome, évidement spontané du tympanal.