[An 8-finger hand with ulnar duplication (mirror image deformity)].
The authors present a congenital arm- and hand deformity in a four year old boy. This "mirror deformity" includes aplasia of the radius, doubled carpus and metacarpus, polydactyly (eight fingers) and aplasia of the thumb. The hypoplastic radial four fingers show brachysyndactyly, the whole upper extremity is hypoplastic but both shoulders are normally developed. The elbow has an extension contraction with a range of movement of 20 degrees in the double olecranons. The wrist has a flexion contracture. At first, pollicisation of the third finger of the hypoplastic radial part of the left hand with resection of three hypoplastic fingers was performed. The thenar muscles were reconstructed with interosseous muscles and the flexion contraction corrected by shortening and doubling of the extensor tendons. Preoperative EMG studies demonstrated two ulnar nerves with cross-innervation of the median nerve. The postoperative situation was recorded again by EMG.
D000671:Amputation, Surgical; D002675:Child, Preschool; D004576:Electromyography; D005385:Fingers / Q000002:abnormalities* / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008663:Metacarpus / Q000002:abnormalities; D009048:Motor Skills; D011884:Radius / Q000002:abnormalities; D013933:Thumb / Q000002:abnormalities; D014457:Ulna / Q000002:abnormalities*
Acht-Finger-Hand mit Ulna-Verdoppelung (Spiegelbild-Deformität).