Metachromasia and assay for lysosomal enzymes in skin fibroblasts cultured from patients with cystic fibrosis and controls.
D000135:Acid Phosphatase / Q000378:metabolism; D000293:Adolescent; D000328:Adult; D002478:Cells, Cultured; D002648:Child; D002675:Child, Preschool; D003550:Cystic Fibrosis / Q000201:enzymology* / Q000378:metabolism / Q000473:pathology; D003594:Cytoplasmic Granules; D005260:Female; D005347:Fibroblasts / Q000201:enzymology; D005696:Galactosidases / Q000378:metabolism; D005966:Glucuronidase / Q000378:metabolism; D006025:Glycosaminoglycans / Q000378:metabolism; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008247:Lysosomes / Q000201:enzymology*; D008297:Male; D008722:Methods; D012867:Skin / Q000166:cytology / Q000201:enzymology; D013194:Staining and Labeling; D013429:Sulfatases / Q000378:metabolism; D013997:Time Factors
D006025:Glycosaminoglycans; D000135:Acid Phosphatase; D013429:Sulfatases; D005696:Galactosidases; D005966:Glucuronidase