The existence of an alternative pathway for the degradation of branch-chained fatty acids, and its failure in heredopathia atactica polyneuritiformis (Refsum's disease).
D000818:Animals; D002245:Carbon Dioxide; D005227:Fatty Acids / Q000378:metabolism*; D006168:Guinea Pigs; D006801:Humans; D007668:Kidney / Q000378:metabolism; D008099:Liver / Q000378:metabolism; D008661:Metabolism, Inborn Errors; D009206:Myocardium / Q000378:metabolism; D011817:Rabbits; D051381:Rats; D012035:Refsum Disease / Q000378:metabolism*; D012756:Sheep
D005227:Fatty Acids; D002245:Carbon Dioxide