Proceedings: The defect in Maroteaux-Lamy disease (mucopolysaccharidosis VI, subtype A): deficiency of N-acetylgalactosamine-4-sulfatase.
D000116:Acetylgalactosamine; D003871:Dermatan Sulfate / Q000378:metabolism; D006801:Humans; D009083:Mucopolysaccharidoses / Q000201:enzymology*; D009087:Mucopolysaccharidosis VI / Q000201:enzymology*; D013429:Sulfatases / Q000172:deficiency*
D003871:Dermatan Sulfate; D013429:Sulfatases; D000116:Acetylgalactosamine