Mucopolysaccharidosis type VI (Maroteaux-Lamy syndrome). I. Sulfatase B deficiency in tissues.
D000293:Adolescent; D000328:Adult; D001921:Brain / Q000201:enzymology; D002239:Carbohydrate Metabolism, Inborn Errors / Q000201:enzymology*; D002648:Child; D002675:Child, Preschool; D004586:Electrophoresis; D005347:Fibroblasts / Q000201:enzymology; D006025:Glycosaminoglycans / Q000378:metabolism*; D006801:Humans; D007668:Kidney / Q000201:enzymology; D008099:Liver / Q000201:enzymology; D008297:Male; D013154:Spleen / Q000201:enzymology; D013429:Sulfatases / Q000378:metabolism*
D006025:Glycosaminoglycans; D013429:Sulfatases