Isolation and characterization of keratan sulfates from the liver of a patient with GM1-gangliosidosis type I.
D000818:Animals; D001344:Autopsy; D002239:Carbohydrate Metabolism, Inborn Errors / Q000378:metabolism*; D002417:Cattle; D002850:Chromatography, Gel; D002852:Chromatography, Ion Exchange; D002854:Chromatography, Paper; D002855:Chromatography, Thin Layer; D005690:Galactose / Q000378:metabolism; D005696:Galactosidases / Q000378:metabolism*; D005732:Gangliosides; D005944:Glucosamine / Q000378:metabolism; D006025:Glycosaminoglycans / Q000302:isolation & purification; D006026:Glycoside Hydrolases / Q000378:metabolism; D006801:Humans; D007633:Keratins; D008099:Liver / Q000032:analysis* / Q000201:enzymology / Q000378:metabolism; D008247:Lysosomes / Q000201:enzymology; D010504:Periodic Acid; D011726:Pyridinium Compounds; D012995:Solubility; D013464:Sulfuric Acids / Q000032:analysis
D005732:Gangliosides; D006025:Glycosaminoglycans; D011726:Pyridinium Compounds; D013464:Sulfuric Acids; D010504:Periodic Acid; D007633:Keratins; D005696:Galactosidases; D006026:Glycoside Hydrolases; D005944:Glucosamine; D005690:Galactose