The glycoasparagines in urine of a patient with aspartylglycosaminuria.
The isolation and analysis of 2-acetamido-N-(4'-l-aspartyl)-2-deoxy-beta-d- glucopyranosylamine and 13 higher-molecular-weight derivatives from the urine of a patient with aspartylglycosaminuria is described. Some structural information is presented for nine of these compounds.
D001216:Asparagine / Q000031:analogs & derivatives / Q000652:urine*; D001224:Aspartic Acid / Q000652:urine*; D002849:Chromatography, Gas; D002850:Chromatography, Gel; D002852:Chromatography, Ion Exchange; D004590:Electrophoresis, Paper; D005260:Female; D005944:Glucosamine / Q000652:urine*; D006020:Glycopeptides / Q000652:urine*; D006029:Glycosuria; D006801:Humans; D006863:Hydrogen-Ion Concentration; D008661:Metabolism, Inborn Errors / Q000652:urine*; D008956:Models, Chemical
D006020:Glycopeptides; C007872:glycoasparagines; D001224:Aspartic Acid; D001216:Asparagine; D005944:Glucosamine