Decreased ketogenesis in von Gierke's disease (type I glycogenosis).
D000138:Acidosis / Q000209:etiology; D000293:Adolescent; D001786:Blood Glucose / Q000032:analysis; D002648:Child; D002675:Child, Preschool; D004035:Diet Therapy; D005230:Fatty Acids, Nonesterified / Q000097:blood; D005260:Female; D005953:Glycogen Storage Disease Type I / Q000097:blood / Q000378:metabolism* / Q000628:therapy; D006801:Humans; D006885:Hydroxybutyrates / Q000008:administration & dosage / Q000097:blood; D007223:Infant; D007659:Ketones / Q000096:biosynthesis* / Q000097:blood / Q000378:metabolism / Q000652:urine; D008297:Male; D014280:Triglycerides / Q000378:metabolism
D001786:Blood Glucose; D005230:Fatty Acids, Nonesterified; D006885:Hydroxybutyrates; D007659:Ketones; D014280:Triglycerides