Additional deficiency of psychosine galactosidase in globoid cell leukodystrophy: an implication to enzyme replacement therapy.
D000818:Animals; D001921:Brain / Q000201:enzymology / Q000378:metabolism; D002250:Carbon Radioisotopes; D002554:Cerebrosides / Q000378:metabolism; D055598:Chemical Phenomena; D002621:Chemistry; D005690:Galactose / Q000378:metabolism; D005696:Galactosidases / Q000032:analysis / Q000172:deficiency* / Q000627:therapeutic use; D007668:Kidney / Q000201:enzymology; D007965:Leukodystrophy, Globoid Cell / Q000188:drug therapy* / Q000201:enzymology / Q000378:metabolism; D008099:Liver / Q000201:enzymology; D051381:Rats
D002250:Carbon Radioisotopes; D002554:Cerebrosides; D005696:Galactosidases; D005690:Galactose