Deficiency of monogalactosyl diglycerid beta-B-galactosidase activity in krabbe's disease.
D001921:Brain / Q000201:enzymology; D002478:Cells, Cultured; D002554:Cerebrosides; D002549:Diffuse Cerebral Sclerosis of Schilder / Q000201:enzymology / Q000235:genetics*; D005347:Fibroblasts / Q000201:enzymology; D005690:Galactose; D005696:Galactosidases / Q000378:metabolism*; D005959:Glucosidases / Q000378:metabolism; D005989:Glycerides; D006801:Humans; D007223:Infant; D008099:Liver / Q000201:enzymology; D012867:Skin; D013107:Sphingolipids; D013110:Sphingosine; D014316:Tritium
D002554:Cerebrosides; D005989:Glycerides; D013107:Sphingolipids; D014316:Tritium; D005696:Galactosidases; D005959:Glucosidases; D013110:Sphingosine; D005690:Galactose