Structure of the "keratosulfate-like" material in liver from a patient with G M1 -gangliosidosis ( -D-galactosidase deficiency).
D000596:Amino Acids / Q000032:analysis; D001344:Autopsy; D002239:Carbohydrate Metabolism, Inborn Errors / Q000201:enzymology*; D002241:Carbohydrates / Q000032:analysis; D055598:Chemical Phenomena; D002621:Chemistry; D002849:Chromatography, Gas; D002850:Chromatography, Gel; D002852:Chromatography, Ion Exchange; D002854:Chromatography, Paper; D005696:Galactosidases / Q000378:metabolism*; D006020:Glycopeptides / Q000032:analysis; D006801:Humans; D007223:Infant; D007633:Keratins / Q000032:analysis*; D008099:Liver / Q000032:analysis* / Q000473:pathology
D000596:Amino Acids; D002241:Carbohydrates; D006020:Glycopeptides; D007633:Keratins; D005696:Galactosidases