Defective metabolic clearance of plasma arginine and ornithine in lysinuric protein intolerance.
D000293:Adolescent; D000328:Adult; D000592:Amino Acid Metabolism, Inborn Errors; D001120:Arginine / Q000097:blood / Q000378:metabolism* / Q000652:urine; D002648:Child; D002675:Child, Preschool; D003553:Cystine / Q000378:metabolism; D003555:Cystinuria / Q000378:metabolism; D005215:Fasting; D005260:Female; D006801:Humans; D007223:Infant; D007263:Infusions, Parenteral; D007674:Kidney Diseases / Q000378:metabolism; D008107:Liver Diseases / Q000378:metabolism; D008239:Lysine / Q000097:blood / Q000652:urine*; D008297:Male; D008657:Metabolic Clearance Rate; D009952:Ornithine / Q000097:blood / Q000378:metabolism* / Q000652:urine; D011507:Proteinuria / Q000235:genetics / Q000378:metabolism; D015499:Renal Tubular Transport, Inborn Errors / Q000378:metabolism; D014508:Urea / Q000096:biosynthesis
D003553:Cystine; D014508:Urea; D001120:Arginine; D009952:Ornithine; D008239:Lysine