A block in glycine cleavage reaction as a common mechanism in ketotic and nonketotic hyperglycinemia.
D000138:Acidosis / Q000150:complications / Q000201:enzymology*; D000592:Amino Acid Metabolism, Inborn Errors / Q000150:complications / Q000201:enzymology*; D002250:Carbon Radioisotopes; D002675:Child, Preschool; D005260:Female; D005998:Glycine / Q000097:blood / Q000378:metabolism*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008099:Liver / Q000201:enzymology; D012694:Serine; D014166:Transferases / Q000378:metabolism
D002250:Carbon Radioisotopes; D012694:Serine; D014166:Transferases; D005998:Glycine