Congenital disorders of the urea cycle and ammonia detoxication.
D000592:Amino Acid Metabolism, Inborn Errors / Q000201:enzymology / Q000235:genetics; D000641:Ammonia / Q000097:blood / Q000378:metabolism* / Q000633:toxicity; D000818:Animals; D001921:Brain / Q000378:metabolism; D002869:Chromosome Aberrations; D005333:Fetus / Q000378:metabolism*; D006801:Humans; D008099:Liver / Q000378:metabolism; D008239:Lysine / Q000378:metabolism; D008661:Metabolism, Inborn Errors / Q000201:enzymology; D014508:Urea / Q000096:biosynthesis / Q000378:metabolism*
D000641:Ammonia; D014508:Urea; D008239:Lysine