Isolation and identification of methylcitrate, a major metabolic product of propionate in patients with propionic acidemia.
D000143:Acids / Q000652:urine; D002247:Carbon Isotopes; D002845:Chromatography; D002849:Chromatography, Gas; D002854:Chromatography, Paper; D002951:Citrates / Q000138:chemical synthesis / Q000302:isolation & purification / Q000652:urine*; D003065:Coenzyme A / Q000378:metabolism; D006801:Humans; D008314:Malonates / Q000652:urine; D013058:Mass Spectrometry; D008661:Metabolism, Inborn Errors / Q000209:etiology / Q000652:urine*; D010071:Oxaloacetates / Q000378:metabolism; D011422:Propionates / Q000097:blood* / Q000378:metabolism
D000143:Acids; D002247:Carbon Isotopes; D002951:Citrates; D008314:Malonates; D010071:Oxaloacetates; D011422:Propionates; D003065:Coenzyme A