The oxidation of glycine and propionic acid in propionic acidemia with ketotic hyperglycinemia.
D000138:Acidosis / Q000097:blood / Q000378:metabolism*; D001826:Body Fluids / Q000032:analysis; D002245:Carbon Dioxide / Q000096:biosynthesis; D002247:Carbon Isotopes; D002675:Child, Preschool; D005260:Female; D005347:Fibroblasts / Q000201:enzymology; D005998:Glycine / Q000097:blood / Q000378:metabolism*; D006801:Humans; D007223:Infant; D007651:Keto Acids / Q000097:blood*; D008025:Ligases / Q000378:metabolism; D008297:Male; D008314:Malonates / Q000097:blood; D010084:Oxidation-Reduction; D011422:Propionates / Q000097:blood / Q000378:metabolism*; D012694:Serine / Q000096:biosynthesis
D002247:Carbon Isotopes; D007651:Keto Acids; D008314:Malonates; D011422:Propionates; D002245:Carbon Dioxide; D012694:Serine; D008025:Ligases; D005998:Glycine