Branching enzyme-deficiency glycogenosis: studies in therapy.
D000328:Adult; D002239:Carbohydrate Metabolism, Inborn Errors; D002675:Child, Preschool; D004035:Diet Therapy; D005260:Female; D005632:Fructose / Q000378:metabolism; D005690:Galactose / Q000378:metabolism; D005934:Glucagon / Q000378:metabolism / Q000627:therapeutic use*; D005951:Glucose Tolerance Test; D005959:Glucosidases / Q000627:therapeutic use*; D006003:Glycogen / Q000378:metabolism; D006008:Glycogen Storage Disease / Q000175:diagnosis / Q000188:drug therapy* / Q000235:genetics; D006026:Glycoside Hydrolases / Q000378:metabolism*; D006801:Humans; D007223:Infant; D007962:Leukocytes / Q000201:enzymology; D008112:Liver Glycogen / Q000032:analysis; D008297:Male; D015032:Zinc / Q000627:therapeutic use*
D008112:Liver Glycogen; D005632:Fructose; D006003:Glycogen; D005934:Glucagon; D005959:Glucosidases; D006026:Glycoside Hydrolases; D015032:Zinc; D005690:Galactose