Simultaneous absence of alpha-1,4-glucosidase and alpha-1,6-glucosidase activities (pH 4) in tissues of children with type II glycogen storage disease.
D001344:Autopsy; D001706:Biopsy; D002648:Child; D046508:Culture Techniques; D004187:Disaccharides; D004355:Drug Stability; D005347:Fibroblasts / Q000201:enzymology; D005959:Glucosidases / Q000037:antagonists & inhibitors / Q000378:metabolism*; D006003:Glycogen; D006008:Glycogen Storage Disease / Q000201:enzymology*; D006026:Glycoside Hydrolases / Q000378:metabolism; D006027:Glycosides; D006801:Humans; D006863:Hydrogen-Ion Concentration; D007700:Kinetics; D007962:Leukocytes / Q000201:enzymology; D008099:Liver / Q000201:enzymology*; D008247:Lysosomes / Q000201:enzymology; D008320:Maltose; D009132:Muscles / Q000201:enzymology*; D009206:Myocardium / Q000201:enzymology
D004187:Disaccharides; D006027:Glycosides; D008320:Maltose; D006003:Glycogen; D005959:Glucosidases; D006026:Glycoside Hydrolases