Familial polyposis coli associated with extracolonic abnormalities.
The pedigree of a polyposis coli family, in which several individuals had extracolonic abnormalities associated with the condition, is presented. Some of the problems encountered in management are discussed. The literature is reviewed and a simple classification of the extracolonic abnormalities is suggested.
D000008:Abdominal Neoplasms / Q000473:pathology; D000328:Adult; D014670:Ampulla of Vater / Q000473:pathology; D001650:Bile Duct Neoplasms / Q000473:pathology; D003110:Colonic Neoplasms / Q000235:genetics* / Q000473:pathology*; D004814:Epidermal Cyst / Q000473:pathology; D005260:Female; D005350:Fibroma / Q000473:pathology; D006222:Hamartoma / Q000473:pathology; D006801:Humans; D007414:Intestinal Neoplasms / Q000473:pathology; D007417:Intestinal Polyps / Q000235:genetics* / Q000473:pathology*; D008297:Male; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary; D010190:Pancreatic Neoplasms / Q000473:pathology