Accumulation of lysine dipeptides in the brain in hyperpipecolatemia.
D000592:Amino Acid Metabolism, Inborn Errors / Q000378:metabolism*; D000596:Amino Acids / Q000032:analysis / Q000378:metabolism; D000818:Animals; D001344:Autopsy; D001921:Brain / Q000378:metabolism* / Q000473:pathology; D001923:Brain Chemistry; D002458:Cell Fractionation; D002493:Central Nervous System Diseases / Q000378:metabolism; D002852:Chromatography, Ion Exchange; D002854:Chromatography, Paper; D004151:Dipeptides / Q000378:metabolism; D006801:Humans; D008099:Liver / Q000378:metabolism; D008239:Lysine / Q000378:metabolism*; D010875:Pipecolic Acids / Q000378:metabolism*; D051381:Rats; D014020:Tissue Extracts
D000596:Amino Acids; D004151:Dipeptides; D010875:Pipecolic Acids; D014020:Tissue Extracts; D008239:Lysine