Beta mercaptolactate-cysteine disulfide: analog of cystine in the urine of a mentally retarded patient.
beta-Mercaptolactate-cysteine disulfide, a hitherto undescribed analog of cystine, was isolated from the urine of a mentally retarded patient. The propertis of this substance are described, and its structure is confirmed by mass spectrometry and by partial synthesis.
D000592:Amino Acid Metabolism, Inborn Errors / Q000652:urine*; D002624:Chemistry, Clinical; D002852:Chromatography, Ion Exchange; D003486:Cyanides; D003545:Cysteine; D003553:Cystine; D004586:Electrophoresis; D005295:Ferrocyanides; D006801:Humans; D007202:Indicators and Reagents; D008607:Intellectual Disability / Q000652:urine*; D007773:Lactates / Q000652:urine; D008875:Middle Aged; D013057:Spectrum Analysis; D013438:Sulfhydryl Compounds / Q000652:urine*
D003486:Cyanides; D005295:Ferrocyanides; D007202:Indicators and Reagents; D007773:Lactates; D013438:Sulfhydryl Compounds; D003553:Cystine; D003545:Cysteine