Lethal complications of the Ehlers-Danlos syndrome.
Death from arterial bleeding or gastrointestinal perforation has previously been reported in more than 15 patients with the Ehlers-Danlos syndrome. On a basis of 100 personally examined patients and a review of published accounts, these events seem particularly likely to occur in two distinct and recognizable forms (the gravis and the ecchymotic forms) of the syndrome.
D000293:Adolescent; D000328:Adult; D002648:Child; D004438:Ecchymosis / Q000150:complications; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000175:diagnosis / Q000235:genetics; D005260:Female; D005767:Gastrointestinal Diseases / Q000150:complications; D006470:Hemorrhage / Q000150:complications; D006801:Humans; D007416:Intestinal Perforation / Q000150:complications; D008297:Male; D008875:Middle Aged; D011379:Prognosis