Dysplasia of the systemic and pulmonary arterial system with tortuosity and lengthening of the arteries. A new entity, diagnosed during life, and leading to coronary death in early childhood.
D000367:Age Factors; D001011:Aorta / Q000473:pathology; D001158:Arteries / Q000002:abnormalities* / Q000473:pathology; D003327:Coronary Disease / Q000209:etiology* / Q000401:mortality; D003331:Coronary Vessels / Q000473:pathology; D006801:Humans; D007223:Infant; D008297:Male; D009206:Myocardium / Q000473:pathology; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000473:pathology; D011666:Pulmonary Valve Stenosis / Q000401:mortality