Familial progressive sensorineural deafness.
D000368:Aged; D001299:Audiometry; D003051:Cochlea / Q000002:abnormalities*; D003638:Deafness / Q000235:genetics*; D007758:Ear, Inner / Q000473:pathology; D004432:Ear, Middle / Q000473:pathology; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D013701:Temporal Bone / Q000473:pathology