The isolation and identification of N-isovalerylglycine from urine of patients with isovaleric acidemia.
D000138:Acidosis; D000596:Amino Acids / Q000378:metabolism* / Q000652:urine*; D002624:Chemistry, Clinical; D002648:Child; D002675:Child, Preschool; D002849:Chromatography, Gas; D003065:Coenzyme A / Q000378:metabolism; D005260:Female; D006801:Humans; D066298:In Vitro Techniques; D007930:Leucine / Q000378:metabolism*; D009682:Magnetic Resonance Spectroscopy; D008297:Male; D013057:Spectrum Analysis; D014631:Valerates
D000596:Amino Acids; D014631:Valerates; D007930:Leucine; D003065:Coenzyme A