Further observations on the biochemical lesion in maple syrup urine disease.
D000818:Animals; D002245:Carbon Dioxide; D002247:Carbon Isotopes; D002262:Carboxy-Lyases / Q000378:metabolism; D002540:Cerebral Cortex / Q000201:enzymology*; D005971:Glutamates / Q000378:metabolism; D006801:Humans; D066298:In Vitro Techniques; D007651:Keto Acids / Q000378:metabolism; D008099:Liver / Q000201:enzymology*; D008375:Maple Syrup Urine Disease / Q000378:metabolism*; D010101:Oxygen Consumption; D011773:Pyruvates / Q000378:metabolism; D051381:Rats
D002247:Carbon Isotopes; D005971:Glutamates; D007651:Keto Acids; D011773:Pyruvates; D002245:Carbon Dioxide; D002262:Carboxy-Lyases