Enzymes of urea synthesis in familial protein intolerance with deficient transport of basic amino acids.
D000592:Amino Acid Metabolism, Inborn Errors / Q000201:enzymology*; D001119:Arginase / Q000378:metabolism*; D001120:Arginine / Q000097:blood; D002648:Child; D004044:Dietary Proteins; D006801:Humans; D008025:Ligases / Q000378:metabolism*; D008099:Liver / Q000201:enzymology; D008190:Lyases / Q000378:metabolism*; D008239:Lysine / Q000097:blood; D009954:Ornithine Carbamoyltransferase / Q000097:blood*; D000608:Renal Aminoacidurias / Q000235:genetics*; D014508:Urea / Q000096:biosynthesis*
D004044:Dietary Proteins; D014508:Urea; D001120:Arginine; D009954:Ornithine Carbamoyltransferase; D001119:Arginase; D008190:Lyases; D008025:Ligases; D008239:Lysine